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owl:Thing yago:IllHealth114052046 yago:Condition113920835 yago:Illness114061805 yago:WikicatCardiogeneticDisorders yago:State100024720 yago:PathologicalState114051917 yago:Disorder114052403 dbo:Disease yago:Abstraction100002137 yago:PhysicalCondition114034177 yago:Disease114070360 yago:Attribute100024264 yago:WikicatCytoskeletalDefects yago:Defect114464005 umbel-rc:AilmentCondition yago:Imperfection114462666 wikidata:Q12136
rdfs:label
Cardiomiopatia dilatativa Dilatační kardiomyopatie Miocardiopatía dilatada 扩张型心肌病 Дилатационная кардиомиопатия Kardiomiopati dilatasi Kardiomiopatia rozstrzeniowa Dilated cardiomyopathy Cardiomyopathie dilatée Cardiomiopatia dilatada Дилатаційна кардіоміопатія 확장성 심근병증 اعتلال عضلة القلب التوسعي Dilatative Kardiomyopathie
rdfs:comment
확장성 심근병증(擴張性心筋病症, dilated cardiomyopathy, DCM)은 심장이 확장하여 피를 효율적으로 내보내지 못하는 질병을 말한다. 확장성 심장근육병증, 확장형 심근병증, 확장성 심근증, 확장성 심근병으로도 부른다. 심장 기능이 감소하여 허파, 간, 기타 신체 체계에 영향을 미칠 수 있다. 확장성 심근병증은 주로 심근에 영향을 미치는 질병군인 심근증의 하나이다. 각기 다른 심근증은 각기 다른 병인이 있으며 각기 다른 방식으로 심장에 영향을 준다. 확장성 심근병증의 경우 심근의 일부가 확장하며, 종종 명백한 원인이 없는 경우가 있다. ينبغي عدم الخلط مع اعتلال عضلة القلب الضخامي أو أي اعتلال آخر لعضلة القلب. (DCM)اعتلال عضلة القلب المتوسعة هي حالة يصبح فيها القلب متوسعاً ولايمكنه ضح الدم بكفاءة. تناقص وظيفة القلب يمكن أن يؤثر على وظيفة الرئتين والكبد وسائر أجهزة الجسم.اعتلال عضلة القلب المتوسعة هو واحد من اعتلالات عضلة القلب وهي مجموعة من الأمراض التي تؤثر على القلب في المقام الأول (عضلة القلب). اعتلالات عضلة القلب المختلفة لديها أسباب مختلفة، وتؤثر على القلب بطرق مختلفة. في اعتلال عضلة القلب المتوسعة جزء من عضلة القلب يصبح متوسعاً، وكثيراً ما يحدث دون أي سبب واضح. وظيفة البطين الأيسر أو الأيمن مضخة القلب الانقباضية تضعف، مما يؤدي إلى توسع عضلة القلب تدريجياً وتضخمها، عملية تسمى إعادة العرض. 扩张性心肌病(英語:Dilated cardiomyopathy、簡稱DCM),也称充血性心肌病,表现为心脏功能减弱,各心腔扩大,不能充分泵血。心脏功能的减弱也会影响肺、肝和其它器官。 扩张性心肌病是心肌病的一种,主要是心肌功能受到影响。不同的心肌病都有各自影响心脏正常功能的原因。患者的一部分心肌细胞膨大,而且没有明显原因。左右心室其一或兩者的收缩泵血功能受损,导致了进一步的心脏肥大。扩张性心肌病作为一种常见的心肌病,男性发病频率高于女性,发病年龄主要集中于20到60岁。三分之一的充血性心力衰竭(CHF)患者是由于患有扩张性心肌病,這個疾病在儿童甚至初生嬰兒中也有发现。 Dilated cardiomyopathy (DCM) is a condition in which the heart becomes enlarged and cannot pump blood effectively. Symptoms vary from none to feeling tired, leg swelling, and shortness of breath. It may also result in chest pain or fainting. Complications can include heart failure, heart valve disease, or an irregular heartbeat. About 1 per 2,500 people is affected. It occurs more frequently in men than women. Onset is most often in middle age. Five-year survival rate is about 50%. It can also occur in children and is the most common type of cardiomyopathy in this age group. Una cardiopatía dilatada (MCD), anteriormente llamada cardiomiopatía congestiva, es un trastorno caracterizado por una hipertrofia y dilatación progresiva del corazón causando debilidad a tal punto de disminuir la capacidad de bombear sangre eficazmente. Esa disminución de la función cardíaca puede afectar a los pulmones y otros órganos y sistemas del cuerpo. Dilatační kardiomyopatie či dilatovaná kardiomypatie, česky městnavá kardiomyopatie, je onemocnění myokardu charakterizované rozšířením srdečních oddílů, což způsobuje sníženou ejekční funkci levé nebo obou komor jako pumpy. Představuje jeden z typů kardiomyopatie, postižení srdečního svalu doprovázené poruchou srdeční funkce. Une cardiomyopathie dilatée (CMD) est une forme de cardiomyopathie (litt. : maladie du muscle cardiaque) dans laquelle les cavités cardiaques - principalement les ventricules - sont dilatées, diminuant de façon significative la capacité du muscle cardiaque à assurer sa fonction de « pompe », conduisant ainsi à l'insuffisance cardiaque et couplé à un risque de mort subite, quel que soit le stade de la maladie. Une cause ischémique (séquelles d'un infarctus du myocarde ou conséquence d'atteintes sévères des artères coronaires) est habituellement exclue de cette entité. Дилатационная кардиомиопатия (ДКМП) — заболевание миокарда, характеризующееся развитием дилатации (растяжения) полостей сердца, с возникновением , но без увеличения толщины стенок. Характерно развитие прогрессирующей сердечной недостаточности, нарушений сердечного ритма и проводимости, тромбоэмболий, внезапной смерти. Критерием заболевания считается снижение фракции выброса левого желудочка ниже 45 % и размер полости левого желудочка в диастолу более 6 см. Kardiomiopati dilatasi adalah suatu kondisi saat jantung menjadi lebih besar dan tidak dapat lagi memompa darah secara efisien. Gejala kardiomiopati dilatasi ini bervariasi mulai dari tidak ada gejala sama sekali, hingga adanya sesak napas, kelelahan, bengkak di kaki, pingsan, dan nyeri dada. Die dilatative Kardiomyopathie (DCM) ist eine krankhafte Erweiterung (Dilatation) des Herzmuskels, besonders des linken Ventrikels. Durch einen systolischen Pumpfehler kommt es zum fortschreitenden Verlust der Auswurfleistung. Hinzu kommt meist auch eine Störung der diastolischen Funktion (diastolische Herzinsuffizienz). Die Erkrankung ist auch in der Veterinärmedizin bekannt, dort allerdings meist erblich. Siehe dazu Dilatative Kardiomyopathie (Veterinärmedizin) Cardiomiopatia dilatada ou miocardiopatia congestiva é uma doença do músculo cardíaco caracterizada por uma dilatação das câmaras ventriculares, gerando progressiva redução da capacidade de bombear sangue pelo ventrículo esquerdo ou por ambos ventrículos, que ocorre sem outra doença que possa explicar as modificações estruturais e funcionais cardíacas. É mais comum em homens de 20 a 60 anos. Quando ocorre 6 meses antes ou após o parto é chamada de miocardiopatia periparto. Дилатаційна кардіоміопатія (застійна міокардіопатія) (ДКМП) — захворювання міокарду з вираженим порушенням насосної функції серця та дилатацією (розширенням) обох шлуночків. La cardiomiopatia dilatativa (detta anche miocardiopatia dilatativa e in passato miocardiopatia congestizia) è una condizione patologica del cuore che si manifesta con la dilatazione ventricolare e la compromissione della funzione sistolica. Kardiomiopatia rozstrzeniowa (łac. cardiomyopathia dilatativa), kardiomiopatia zastoinowa (łac. cardiomyopathia congestiva), kardiomiopatia przekrwienna – choroba mięśnia sercowego polegająca na jego ścieńczeniu, zwłaszcza w obrębie komór. Następuje wybiórcze powiększenie jąder bez przerostu komórki oraz zwłóknienie śródmiąższowe i okołonaczyniowe. Podobny obraz można spotkać w kardiomiopatii wtórnej, czyli na tle zapalenia mięśnia sercowego, co utrudnia postawienie właściwej diagnozy. Kardiomiopatia rozstrzeniowa powoduje zmniejszenie kurczliwości serca, co prowadzi najpierw do powstania lewokomorowej niewydolności tego mięśnia, a następnie do jego niewydolności obukomorowej. Rozstrzeń dotyka często także oba przedsionki. Przerost jest z reguły asymetryczny.
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Dilated cardiomyopathy
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Dilated cardiomyopathy
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Tachycardia-induced, others
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Supported by electrocardiogram, chest X-ray, echocardiogram
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Middle age
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Feeling tired, leg swelling, shortness of breath, chest pain, fainting
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Lifestyle changes, medications, implantable cardioverter defibrillator, cardiac resynchronization therapy , heart transplant
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Mouse heart slice showing dilated cardiomyopathy
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Genetics, alcohol, cocaine, certain toxins, complications of pregnancy, in many cases the cause remains unclear, certain infections
dbp:date
2013-05-25
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dbr:Cardiology
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1
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Congestive cardiomyopathy, primary cardiomyopathy idiopathic cardiomyopathy,
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n18:
dbo:abstract
Kardiomiopatia rozstrzeniowa (łac. cardiomyopathia dilatativa), kardiomiopatia zastoinowa (łac. cardiomyopathia congestiva), kardiomiopatia przekrwienna – choroba mięśnia sercowego polegająca na jego ścieńczeniu, zwłaszcza w obrębie komór. Następuje wybiórcze powiększenie jąder bez przerostu komórki oraz zwłóknienie śródmiąższowe i okołonaczyniowe. Podobny obraz można spotkać w kardiomiopatii wtórnej, czyli na tle zapalenia mięśnia sercowego, co utrudnia postawienie właściwej diagnozy. Kardiomiopatia rozstrzeniowa powoduje zmniejszenie kurczliwości serca, co prowadzi najpierw do powstania lewokomorowej niewydolności tego mięśnia, a następnie do jego niewydolności obukomorowej. Rozstrzeń dotyka często także oba przedsionki. Przerost jest z reguły asymetryczny. Cardiomiopatia dilatada ou miocardiopatia congestiva é uma doença do músculo cardíaco caracterizada por uma dilatação das câmaras ventriculares, gerando progressiva redução da capacidade de bombear sangue pelo ventrículo esquerdo ou por ambos ventrículos, que ocorre sem outra doença que possa explicar as modificações estruturais e funcionais cardíacas. É mais comum em homens de 20 a 60 anos. Quando ocorre 6 meses antes ou após o parto é chamada de miocardiopatia periparto. La cardiomiopatia dilatativa (detta anche miocardiopatia dilatativa e in passato miocardiopatia congestizia) è una condizione patologica del cuore che si manifesta con la dilatazione ventricolare e la compromissione della funzione sistolica. 확장성 심근병증(擴張性心筋病症, dilated cardiomyopathy, DCM)은 심장이 확장하여 피를 효율적으로 내보내지 못하는 질병을 말한다. 확장성 심장근육병증, 확장형 심근병증, 확장성 심근증, 확장성 심근병으로도 부른다. 심장 기능이 감소하여 허파, 간, 기타 신체 체계에 영향을 미칠 수 있다. 확장성 심근병증은 주로 심근에 영향을 미치는 질병군인 심근증의 하나이다. 각기 다른 심근증은 각기 다른 병인이 있으며 각기 다른 방식으로 심장에 영향을 준다. 확장성 심근병증의 경우 심근의 일부가 확장하며, 종종 명백한 원인이 없는 경우가 있다. Dilatační kardiomyopatie či dilatovaná kardiomypatie, česky městnavá kardiomyopatie, je onemocnění myokardu charakterizované rozšířením srdečních oddílů, což způsobuje sníženou ejekční funkci levé nebo obou komor jako pumpy. Představuje jeden z typů kardiomyopatie, postižení srdečního svalu doprovázené poruchou srdeční funkce. Una cardiopatía dilatada (MCD), anteriormente llamada cardiomiopatía congestiva, es un trastorno caracterizado por una hipertrofia y dilatación progresiva del corazón causando debilidad a tal punto de disminuir la capacidad de bombear sangre eficazmente. Esa disminución de la función cardíaca puede afectar a los pulmones y otros órganos y sistemas del cuerpo. Une cardiomyopathie dilatée (CMD) est une forme de cardiomyopathie (litt. : maladie du muscle cardiaque) dans laquelle les cavités cardiaques - principalement les ventricules - sont dilatées, diminuant de façon significative la capacité du muscle cardiaque à assurer sa fonction de « pompe », conduisant ainsi à l'insuffisance cardiaque et couplé à un risque de mort subite, quel que soit le stade de la maladie. Une cause ischémique (séquelles d'un infarctus du myocarde ou conséquence d'atteintes sévères des artères coronaires) est habituellement exclue de cette entité. Cette dernière est la forme la plus courante de cardiomyopathie. Dilated cardiomyopathy (DCM) is a condition in which the heart becomes enlarged and cannot pump blood effectively. Symptoms vary from none to feeling tired, leg swelling, and shortness of breath. It may also result in chest pain or fainting. Complications can include heart failure, heart valve disease, or an irregular heartbeat. Causes include genetics, alcohol, cocaine, certain toxins, complications of pregnancy, and certain infections. Coronary artery disease and high blood pressure may play a role, but are not the primary cause. In many cases the cause remains unclear. It is a type of cardiomyopathy, a group of diseases that primarily affects the heart muscle. The diagnosis may be supported by an electrocardiogram, chest X-ray, or echocardiogram. In those with heart failure, treatment may include medications in the ACE inhibitor, beta blocker, and diuretic families. A low salt diet may also be helpful. In those with certain types of irregular heartbeat, blood thinners or an implantable cardioverter defibrillator may be recommended. Cardiac resynchronization therapy (CRT) may be necessary. If other measures are not effective a heart transplant may be an option in some. About 1 per 2,500 people is affected. It occurs more frequently in men than women. Onset is most often in middle age. Five-year survival rate is about 50%. It can also occur in children and is the most common type of cardiomyopathy in this age group. Дилатационная кардиомиопатия (ДКМП) — заболевание миокарда, характеризующееся развитием дилатации (растяжения) полостей сердца, с возникновением , но без увеличения толщины стенок. Характерно развитие прогрессирующей сердечной недостаточности, нарушений сердечного ритма и проводимости, тромбоэмболий, внезапной смерти. Критерием заболевания считается снижение фракции выброса левого желудочка ниже 45 % и размер полости левого желудочка в диастолу более 6 см. Kardiomiopati dilatasi adalah suatu kondisi saat jantung menjadi lebih besar dan tidak dapat lagi memompa darah secara efisien. Gejala kardiomiopati dilatasi ini bervariasi mulai dari tidak ada gejala sama sekali, hingga adanya sesak napas, kelelahan, bengkak di kaki, pingsan, dan nyeri dada. Penyebab kardiomiopati dilatasi ini antara lain genetik, kokain, alkohol, toksin tertentu, komplikasi dari kehamilan, dan infeksi tertentu. Tekanan darah tinggi dan penyakit jantung koroner mungkin saja berperan dalam situasi ini, tetapi itu bukanlah alasan utama. Dalam kebanyakan kasus, penyebabnya masih belum jelas (idiopatik). Diagnosis dapat didukung oleh rontgen toraks, elektrokardiogram, atau ekokardiogram. 扩张性心肌病(英語:Dilated cardiomyopathy、簡稱DCM),也称充血性心肌病,表现为心脏功能减弱,各心腔扩大,不能充分泵血。心脏功能的减弱也会影响肺、肝和其它器官。 扩张性心肌病是心肌病的一种,主要是心肌功能受到影响。不同的心肌病都有各自影响心脏正常功能的原因。患者的一部分心肌细胞膨大,而且没有明显原因。左右心室其一或兩者的收缩泵血功能受损,导致了进一步的心脏肥大。扩张性心肌病作为一种常见的心肌病,男性发病频率高于女性,发病年龄主要集中于20到60岁。三分之一的充血性心力衰竭(CHF)患者是由于患有扩张性心肌病,這個疾病在儿童甚至初生嬰兒中也有发现。 Die dilatative Kardiomyopathie (DCM) ist eine krankhafte Erweiterung (Dilatation) des Herzmuskels, besonders des linken Ventrikels. Durch einen systolischen Pumpfehler kommt es zum fortschreitenden Verlust der Auswurfleistung. Hinzu kommt meist auch eine Störung der diastolischen Funktion (diastolische Herzinsuffizienz). Die Erkrankung ist auch in der Veterinärmedizin bekannt, dort allerdings meist erblich. Siehe dazu Dilatative Kardiomyopathie (Veterinärmedizin) ينبغي عدم الخلط مع اعتلال عضلة القلب الضخامي أو أي اعتلال آخر لعضلة القلب. (DCM)اعتلال عضلة القلب المتوسعة هي حالة يصبح فيها القلب متوسعاً ولايمكنه ضح الدم بكفاءة. تناقص وظيفة القلب يمكن أن يؤثر على وظيفة الرئتين والكبد وسائر أجهزة الجسم.اعتلال عضلة القلب المتوسعة هو واحد من اعتلالات عضلة القلب وهي مجموعة من الأمراض التي تؤثر على القلب في المقام الأول (عضلة القلب). اعتلالات عضلة القلب المختلفة لديها أسباب مختلفة، وتؤثر على القلب بطرق مختلفة. في اعتلال عضلة القلب المتوسعة جزء من عضلة القلب يصبح متوسعاً، وكثيراً ما يحدث دون أي سبب واضح. وظيفة البطين الأيسر أو الأيمن مضخة القلب الانقباضية تضعف، مما يؤدي إلى توسع عضلة القلب تدريجياً وتضخمها، عملية تسمى إعادة العرض. اعتلال عضلة القلب المتوسعة هو الشكل الأكثر شيوعاً لاعتلال عضلة القلب اللاإقفاري. ويحدث ذلك بشكل متكرر أكثر في الرجال عنه من النساء، وهو الأكثر شيوعاً في الذين تتراوح أعمارهم ما بين 20 و60 عاماً. (CHF) حوالي واحدة من بين كل ثلاث حالات فشل القلب الاحتقاني سببها اعتلال عضلة القلب المتوسعة.اعتلال عضلة القلب المتوسعة يحدث أيضاً في الأطفال. Дилатаційна кардіоміопатія (застійна міокардіопатія) (ДКМП) — захворювання міокарду з вираженим порушенням насосної функції серця та дилатацією (розширенням) обох шлуночків.
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Coronary artery disease, heart valve disease, pulmonary embolism, other cardiomyopathy
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Dystrophinopathies
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Dilated Cardiomyopathy Overview
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Five-year survival rate ~50%
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Dilated Cardiomyopathy Overview
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