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- Poikiloderma vasculare atrophicans (PVA), is a cutaneous condition (skin disease) characterized by hypo- or hyperpigmentation (diminished or heightened skin pigmentation, respectively), telangiectasia and skin atrophy. Other names for the condition include prereticulotic poikiloderma and atrophic parapsoriasis. The condition was first described by pioneer American pediatrician Abraham Jacobi in 1906. PVA causes areas of affected skin to appear speckled red and inflamed, yellowish and/or brown, gray or grayish-black, with scaling and a thinness that may be described as "cigarette paper". On the surface of the skin, these areas may range in size from small patches, to plaques (larger, raised areas), to neoplasms (spreading, tumor-like growths on the skin). Mycosis fungoides, a type of skin lymphoma, may be a cause of PVA. The condition may also be caused by, associated with or accompany any of the following conditions or disorders: other skin lymphomas, dermatomyositis, lupus erythematosus, Rothmund–Thomson syndrome, Kindler syndrome, dyskeratosis congenita, and chronic radiodermatitis. Rare causes include arsenic ingestion, and the condition can also be idiopathic. PVA may be considered a rare variant of cutaneous T-cell lymphoma, a non-Hodgkin's form of lymphoma affecting the skin. It may also be included among a number of similar conditions that are considered as precursors to mycosis fungoides. PVA is believed to be a syndrome closely associated with large-plaque parapsoriasis and its cohort retiform parapsoriasis; including PVA, all three conditions fit within an updated view of the once ambiguous classification scheme known as parapsoriasis. (en)
- La poichilodermia vascolare atrofizzante o poikiloderma vasculare atrophicans (PVA) è una condizione patologica della cute caratterizzata da ipopigmentazione o , teleangectasia e atrofia della pelle. Altri nomi di questa patologia sono poichilodermia pre-reticolare e parapsoriasi atrofica. Questa poichilodermia si manifesta con chiazze della pelle che presentano infiammazione e un colorito rossastro, giallastro, marrone, grigio o grigio-nerastro, con un assottigliamento che fa assumere alla cute interessata dalla lesione un tipico aspetto a cartina di sigaretta. A livello dell'epidermide queste aree possono avere una dimensione variabile da piccole macchie a placche rialzate rispetto alla cute circostante; ulteriore possibile degenerazione delle lesioni è la loro estensione incontrollata sotto forma di neoplasia. (it)
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- Typical skin changes and discoloration described as poikiloderma vasculare atrophicans (en)
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- The layers of the epidermis . Melanocytes , located in the bottom epidermal layer, produce melanin. (en)
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- 696.200000 (xsd:double)
- (en)
- L94.5 (en)
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- Illu_skin02.jpg (en)
- Skinlayers.png (en)
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- Poikiloderma vasculare atrophicans (en)
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- Parapsoriasis variegata or Parapsoriasis lichenoides (en)
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- 200 (xsd:integer)
- 250 (xsd:integer)
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- Poikiloderma vasculare atrophicans (PVA), is a cutaneous condition (skin disease) characterized by hypo- or hyperpigmentation (diminished or heightened skin pigmentation, respectively), telangiectasia and skin atrophy. Other names for the condition include prereticulotic poikiloderma and atrophic parapsoriasis. The condition was first described by pioneer American pediatrician Abraham Jacobi in 1906. PVA causes areas of affected skin to appear speckled red and inflamed, yellowish and/or brown, gray or grayish-black, with scaling and a thinness that may be described as "cigarette paper". On the surface of the skin, these areas may range in size from small patches, to plaques (larger, raised areas), to neoplasms (spreading, tumor-like growths on the skin). (en)
- La poichilodermia vascolare atrofizzante o poikiloderma vasculare atrophicans (PVA) è una condizione patologica della cute caratterizzata da ipopigmentazione o , teleangectasia e atrofia della pelle. Altri nomi di questa patologia sono poichilodermia pre-reticolare e parapsoriasi atrofica. Questa poichilodermia si manifesta con chiazze della pelle che presentano infiammazione e un colorito rossastro, giallastro, marrone, grigio o grigio-nerastro, con un assottigliamento che fa assumere alla cute interessata dalla lesione un tipico aspetto a cartina di sigaretta. A livello dell'epidermide queste aree possono avere una dimensione variabile da piccole macchie a placche rialzate rispetto alla cute circostante; ulteriore possibile degenerazione delle lesioni è la loro estensione incontrollata s (it)
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- Poichilodermia vascolare atrofizzante (it)
- Poikiloderma vasculare atrophicans (en)
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- Poikiloderma vasculare atrophicans (en)
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