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Y-linked deafness, type 1 is a very rare type of hereditary non-syndromic deafness characterized by progressive hearing loss that exclusively affects males. It has been described in 42 males from 2 multi-generational Chinese families.

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dbo:abstract
  • Y-linked deafness, type 1 is a very rare type of hereditary non-syndromic deafness characterized by progressive hearing loss that exclusively affects males. It has been described in 42 males from 2 multi-generational Chinese families. (en)
dbo:alias
  • (en)
  • DFNY1 (en)
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dbo:wikiPageID
  • 71427358 (xsd:integer)
dbo:wikiPageLength
  • 7809 (xsd:nonNegativeInteger)
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  • 1108896980 (xsd:integer)
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dbp:caption
  • This condition is one of the few known to be caused by mutations in the Y chromosome. (en)
dbp:causes
dbp:deaths
  • - (en)
dbp:duration
  • Lifelong (en)
dbp:frequency
  • rare, only two extended Chinese families have been described in medical literature (en)
dbp:name
  • Y-linked deafness, type 1 (en)
dbp:onset
  • Variable (en)
dbp:prevention
  • none (en)
dbp:prognosis
  • With support, good (en)
dbp:specialty
dbp:symptoms
  • Progressive hearing impairment that occurs in all male members of a family. (en)
dbp:synonyms
  • DFNY1 (en)
dbp:treatment
  • Common methods such as Cochlear implant or hearing aids (en)
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dcterms:subject
rdf:type
rdfs:comment
  • Y-linked deafness, type 1 is a very rare type of hereditary non-syndromic deafness characterized by progressive hearing loss that exclusively affects males. It has been described in 42 males from 2 multi-generational Chinese families. (en)
rdfs:label
  • Y-linked deafness, type 1 (en)
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