. "186"@en . . . "2191954"^^ . . . . . . . "Lennox-Gastauts syndrom \u00E4r en form av epilepsi som oftast debuterar vid 3 till 5 \u00E5rs \u00E5lder. 15 av 100 000 f\u00F6dda ber\u00E4knas f\u00E5 den. Inl\u00E4rningssv\u00E5righeter, dyslexi och dyskalkyli \u00E4r karakteristiska f\u00F6r denna sjukdom. Vissa av barnen \u00E4r normalbeg\u00E5vade, dock kan sjukdomen kopplas till utvecklingsst\u00F6rning. Fysiska symptom \u00E4r atypiska absenser och s\u00E5 kallade drop-attacker d\u00E4r patienten riskerar fallskador."@sv . "186"^^ . "Lennox\u2013Gastaut syndrome (LGS) is a complex, rare, and severe childhood-onset epilepsy. It is characterized by multiple and concurrent seizure types, cognitive dysfunction, and slow spike waves on electroencephalogram (EEG). Typically, it presents in children aged 3\u20135 years and can persist into adulthood. It has been associated with several gene mutations, perinatal injuries, congenital infections, brain tumors/malformations, and genetic disorders such as tuberous sclerosis and West syndrome. The prognosis for LGS is poor with a 5% mortality in childhood and persistent seizures into adulthood (80%\u201390%). LGS was named for neurologists William G. Lennox (Boston, USA) and Henri Gastaut (Marseille, France), who independently described the condition. The international LGS Awareness Day is on November 1."@en . "Das Lennox-Gastaut-Syndrom (LGS), auch unter dem Synonym Lennox-Syndrom bekannt, ist eine meist schwer behandelbare Form von Epilepsie, die bei Kindern in der Regel in der Zeit zwischen dem zweiten und sechsten Lebensjahr beginnt, mit h\u00E4ufigen und verschiedenen Anfallstypen einhergeht und deren Ursache in einer urs\u00E4chlich vielf\u00E4ltigen Sch\u00E4digung des Gehirns besteht, die entweder vorgeburtlich (pr\u00E4natal), w\u00E4hrend der Geburt (perinatal) oder nachgeburtlich (postnatal) entstanden ist."@de . . . . . . . . . . . . . . . . . . . . . . . "neuro"@en . . . . "29493"^^ . "Generalized 3 Hz spike and wave discharges in a child with childhood absence epilepsy."@en . . . "Lennox\u2013Gastaut syndrome"@en . . . . "Lennox\u2013Gastaut syndrome"@en . . "\u0645\u062A\u0644\u0627\u0632\u0645\u0629 \u0644\u064A\u0646\u0648\u0643\u0633-\u063A\u0627\u0633\u062A\u0648 (LGS) \u0647\u064A \u062D\u0627\u0644\u0629 \u0635\u0631\u0639 \u0628\u062F\u0627\u0626\u064A\u0629 \u0639\u0646\u062F \u0627\u0644\u0623\u0637\u0641\u0627\u0644 \u0648\u062A\u0638\u0647\u0631 \u063A\u0627\u0644\u0628\u0627\u064B \u0639\u0646\u062F \u0627\u0644\u0641\u0626\u0629 \u0627\u0644\u0639\u0645\u0631\u064A\u0629 \u0645\u0646 \u0633\u0646\u062A\u064A\u0646 \u0625\u0644\u0649 \u0633\u062A \u0633\u0646\u0648\u0627\u062A. \u0648\u062A\u062A\u0645\u062B\u0644 \u0628\u062B\u0644\u0627\u062B \u0639\u0644\u0627\u0645\u0627\u062A \u0645\u0646\u0647\u0627 \u0646\u0648\u0628\u0627\u062A \u0635\u0631\u0639 \u0645\u062A\u0639\u062F\u062F\u0629 \u0627\u0644\u0623\u0646\u0648\u0627\u0639 \u0645\u062A\u0643\u0631\u0631\u0629\u060C \u0646\u0645\u0637 \u063A\u064A\u0631 \u0637\u0628\u064A\u0639\u064A \u0645\u0646 \u0645\u0648\u062C\u0627\u062A \u0627\u0644\u062F\u0645\u0627\u063A \u062A\u0643\u0648\u0646 \u0639\u0628\u0627\u0631\u0629 \u0639\u0646 \u0646\u0634\u0627\u0637 \u0645\u0648\u062C\u064A \u0628\u0637\u064A\u0621 \u062A\u0631\u062F\u062F\u0647 \u0623\u0642\u0644 \u0645\u0646 2.5 \u0647\u064A\u0631\u062A\u0632\u060C \u0648\u064A\u062A\u0631\u0627\u0648\u062D \u0627\u0644\u0627\u0639\u062A\u0644\u0627\u0644 \u0627\u0644\u0639\u0642\u0644\u064A \u0641\u064A \u0647\u0630\u0647 \u0627\u0644\u062D\u0627\u0644\u0629 \u0645\u0646 \u0645\u0639\u062A\u062F\u0644 \u0625\u0644\u0649 \u062D\u0627\u062F."@ar . . . . "Zesp\u00F3\u0142 Lennoxa-Gastauta rozwija si\u0119 mi\u0119dzy 1-8 rokiem \u017Cycia, cz\u0119\u015Bciej u ch\u0142opc\u00F3w. W sumie stanowi ok. 5-10% przypadk\u00F3w zespo\u0142\u00F3w padaczkowych u dzieci. Podobnie jak zesp\u00F3\u0142 Westa nale\u017Cy do grupy padaczek lekoopornych. Objawy zespo\u0142u s\u0105 zr\u00F3\u017Cnicowane. Mog\u0105 to by\u0107 napady atoniczne, z nag\u0142\u0105 utrat\u0105 napi\u0119cia mi\u0119\u015Bni i upadkiem, lub te\u017C napady miokloniczne ze skurczem grup mi\u0119\u015Bniowych. W zespole tym mog\u0105 si\u0119 r\u00F3wnie\u017C zdarzy\u0107 miokloniczno-astatyczne objawy b\u0119d\u0105ce po\u0142\u0105czeniem dw\u00F3ch wspomnianych wcze\u015Bniej typ\u00F3w. S\u0105 one przez to do\u015B\u0107 niebezpieczne dla zdrowia a nawet \u017Cycia dziecka, gdy\u017C towarzysz\u0105 im liczne obra\u017Cenia cia\u0142a w trakcie upadku. Ostatnim rodzajem s\u0105 nietypowe napady nie\u015Bwiadomo\u015Bci, z d\u0142u\u017Cszym okresem trwania (>20 sek.), automatyzmami, cz\u0119\u015Bciowymi utratami przytomno\u015Bci. S\u0105 one charakterystyczne dla tego zespo\u0142u. Nast\u0119pstwem tych dochodz\u0105cych do 100/dzie\u0144 napad\u00F3w jest op\u00F3\u017Anienie rozwoju i zaburzenia mowy."@pl . . "\u0645\u062A\u0644\u0627\u0632\u0645\u0629 \u0644\u064A\u0646\u0648\u0643\u0633-\u063A\u0627\u0633\u062A\u0648"@ar . "S\u00EDndrome de Lennox-Gastaut (SLG) ou encefalopatia epil\u00E9tica da inf\u00E2ncia \u00E9 uma s\u00EDndrome epil\u00E9tica pedi\u00E1trica grave que constitui 1 a 4% das epilepsias da inf\u00E2ncia. SLG \u00E9 comumente caracterizada por uma tr\u00EDade de sintomas: epilepsia de v\u00E1rios padr\u00F5es, retardo mental (RM) e complexos ponta-onda lentos no eletroencefalograma (EEG). Os padr\u00F5es de epilepsia mais comuns relacionados \u00E0 s\u00EDndrome s\u00E3o t\u00F4nica axial, at\u00F4nica, e de aus\u00EAncia, mas convuls\u00F5es parciais, miocl\u00F4nicas e t\u00F4nica-cl\u00F4nica generalizadas tamb\u00E9m s\u00E3o observadas."@pt . . . . "1117197948"^^ . . . . . "Het syndroom van Lennox-Gastaut is een kinderepilepsiesyndroom dat zich openbaart bij kinderen van twee tot drie jaar. Pati\u00EBntjes vertonen bij vermoeidheid of beginnende slaap krampaanvallen of vallen met een klap voor- of achterover (drop attacks). Het lichaam spant zich in een boog achterover, de ogen draaien weg en de adem lijkt te stokken."@nl . . "El s\u00EDndrome de Lennox-Gastaut (LGS), tambi\u00E9n conocido como s\u00EDndrome de Lennox, es una variante de epilepsia infantil de dif\u00EDcil manejo, que aparece entre los dos y seis a\u00F1os de vida, y que se caracteriza por convulsiones frecuentes y diversas; a menudo se acompa\u00F1a de discapacidad intelectual y problemas conductuales."@es . . . . . "La sindrome di Lennox-Gastaut (o LGS dalla lingua inglese Lennox\u2013Gastaut syndrome) \u00E8 un'encefalopatia epilettica et\u00E0-dipendente, ad esordio infantile, caratterizzata dalla presenza di crisi polimorfe, farmacoresistenti, associate a deterioramento cognitivo e ad un EEG tipico. \u00C8 classificata come encefalopatia epilettica generalizzata (ILAE 2001)."@it . . "345.0" . . . . "\u30EC\u30CE\u30C3\u30AF\u30B9\u30FB\u30AC\u30B9\u30C8\u30FC\u75C7\u5019\u7FA4\uFF08\u30EC\u30CE\u30C3\u30AF\u30B9\u30FB\u30AC\u30B9\u30C8\u30FC\u3057\u3087\u3046\u3053\u3046\u3050\u3093\u3001Lennox\u2013Gastaut syndrome, LGS\uFF09\u3068\u306F\u3001\u5C0F\u5150\u671F\u306B\u767A\u75C7\u3059\u308B\u96E3\u6CBB\u6027\u306E\u3066\u3093\u304B\u3093\u3067\u3001\u7279\u306B2\u6B73\u304B\u30896\u6B73\u306E\u9593\u306B\u597D\u767A\u3059\u308B\u3002\u591A\u5F69\u306A\u3066\u3093\u304B\u3093\u767A\u4F5C\u304C\u983B\u7E41\u306B\u8D77\u304D\u308B\u3001\u8133\u6CE2\u691C\u67FB\u30672.5 Hz\u672A\u6E80\u306E\u9045\u3044\u304C\u691C\u51FA\u3055\u308C\u308B\u3001\u4E2D\u7B49\u5EA6\u304B\u3089\u91CD\u5EA6\u306E\u7CBE\u795E\u767A\u9054\u9045\u6EDE\u304C\u898B\u3089\u308C\u308B\u3001\u3068\u3044\u30463\u3064\u306E\u5FB4\u5019\u3092\u7279\u5FB4\u3068\u3059\u308B\u3002\u65E5\u672C\u3067\u306F\u6307\u5B9A\u96E3\u75C5144\u306B\u6307\u5B9A\u3055\u308C\u3066\u3044\u308B\u3002"@ja . . . "S\u00EDndrome de Lennox-Gastaut (SLG) ou encefalopatia epil\u00E9tica da inf\u00E2ncia \u00E9 uma s\u00EDndrome epil\u00E9tica pedi\u00E1trica grave que constitui 1 a 4% das epilepsias da inf\u00E2ncia. SLG \u00E9 comumente caracterizada por uma tr\u00EDade de sintomas: epilepsia de v\u00E1rios padr\u00F5es, retardo mental (RM) e complexos ponta-onda lentos no eletroencefalograma (EEG). Os padr\u00F5es de epilepsia mais comuns relacionados \u00E0 s\u00EDndrome s\u00E3o t\u00F4nica axial, at\u00F4nica, e de aus\u00EAncia, mas convuls\u00F5es parciais, miocl\u00F4nicas e t\u00F4nica-cl\u00F4nica generalizadas tamb\u00E9m s\u00E3o observadas."@pt . "Sindrome di Lennox-Gastaut"@it . . . . . . "Syndrome de Lennox-Gastaut"@fr . . . . . "\uB808\uB179\uC2A4-\uAC00\uC2A4\uD1A0 \uC99D\uD6C4\uAD70(Lennox\u2013Gastaut syndrome,LGS)\uC740 \uBCF5\uC7A1\uD558\uACE0 \uB4DC\uBB3C\uACE0 \uC2EC\uD55C \uC544\uB3D9\uAE30 \uBC1C\uC791 \uAC04\uC9C8\uC774\uB2E4. \uC774\uAC83\uC740 \uC5EC\uB7EC \uAC1C\uC758 \uB3D9\uC2DC \uBC1C\uC791 \uC720\uD615\uACFC \uC778\uC9C0 \uAE30\uB2A5 \uC7A5\uC560 \uBC0F \uB1CC\uC804\uB3C4 (EEG) \uB1CC\uD30C\uC758 \uB290\uB9B0 \uC2A4\uD30C\uC774\uD06C \uD30C\uB85C \uD2B9\uC9D5 \uC9C0\uC5B4\uC9C4\uB2E4. \uC77C\uBC18\uC801\uC73C\uB85C 3 ~ 5 \uC138 \uC5B4\uB9B0\uC774\uC5D0\uAC8C\uC11C \uBCF4\uC5EC\uC9C0\uBA70 \uC131\uC778\uC774 \uB420 \uC218 \uC788\uB2E4. \uC5EC\uB7EC \uC720\uC804\uC790 \uB3CC\uC5F0\uBCC0\uC774, \uC8FC\uC0B0\uAE30(\u5468\u7523\u671F) \uBC1C\uB2EC\uC7A5\uC560, \uC120\uCC9C\uC131 \uAC10\uC5FC, \uB1CC\uC885\uC591 / \uBCC0\uD615, (Tuberous sclerosis) \uBC0F (West Syndrome)\uACFC \uAC19\uC740 \uC720\uC804\uC801 \uC7A5\uC560\uC640 \uAD00\uB828\uC774 \uC788\uB2E4. LGS\uC5D0 \uB300\uD55C \uC608\uD6C4\uB294 \uC720\uB144\uAE30 \uC0AC\uB9DD\uB960\uC774 5 %\uC774\uACE0 \uC131\uC778\uC73C\uB85C\uC758 \uC9C0\uC18D\uC801\uC778 \uBC1C\uC791 (80 % -90 %)\uC73C\uB85C \uC88B\uC9C0 \uC54A\uC740 \uAC83\uC73C\uB85C \uC54C\uB824\uC838\uC788\uB2E4. LGS\uB294 \uC2E0\uACBD\uACFC \uC804\uBB38\uC758\uC778 \uC70C\uB9AC\uC5C4 \uB808\uB179\uC2A4(William G. Lennox)\uC640 (Henri Gastaut)\uC758 \uC774\uB984\uC744 \uB530\uB790\uB2E4. LGS\uC5D0\uB300\uD55C \uC778\uC2DD\uC744 \uC704\uD574 \uAD6D\uC81C LGS \uB0A0\uC740 11\uC6D4 1\uC77C\uB2E4."@ko . . . "S\u00EDndrome de Lennox-Gastaut"@es . . . "Lennox-Gastauts syndrom"@sv . . . . "S\u00EDndrome de Lennox-Gastaut"@pt . "Zesp\u00F3\u0142 Lennoxa-Gastauta"@pl . . . . "Das Lennox-Gastaut-Syndrom (LGS), auch unter dem Synonym Lennox-Syndrom bekannt, ist eine meist schwer behandelbare Form von Epilepsie, die bei Kindern in der Regel in der Zeit zwischen dem zweiten und sechsten Lebensjahr beginnt, mit h\u00E4ufigen und verschiedenen Anfallstypen einhergeht und deren Ursache in einer urs\u00E4chlich vielf\u00E4ltigen Sch\u00E4digung des Gehirns besteht, die entweder vorgeburtlich (pr\u00E4natal), w\u00E4hrend der Geburt (perinatal) oder nachgeburtlich (postnatal) entstanden ist."@de . . . "G40.4" . . ""@en . . "\uB808\uB179\uC2A4-\uAC00\uC2A4\uD1A0 \uC99D\uD6C4\uAD70"@ko . . . . . . "neuro"@en . . . "Le syndrome de Lennox-Gastaut, \u00E9galement connu sous le nom de syndrome de Lennox, est une forme d'\u00E9pilepsie infantile difficile \u00E0 traiter qui apparait le plus souvent entre l'\u00E2ge de 2 et 6 ans et qui se caract\u00E9rise par une r\u00E9gression psychomotrice ainsi que des crises fr\u00E9quentes et de types diff\u00E9rents (toniques avec chutes traumatisantes, g\u00E9n\u00E9ralis\u00E9es tonico-cloniques, des crises toniques nocturnes ou des absences atypiques)."@fr . . "29493" . . . . . "2382" . . . "Het syndroom van Lennox-Gastaut is een kinderepilepsiesyndroom dat zich openbaart bij kinderen van twee tot drie jaar. Pati\u00EBntjes vertonen bij vermoeidheid of beginnende slaap krampaanvallen of vallen met een klap voor- of achterover (drop attacks). Het lichaam spant zich in een boog achterover, de ogen draaien weg en de adem lijkt te stokken."@nl . . "Syndroom van Lennox-Gastaut"@nl . . "2382"^^ . . "\u30EC\u30CE\u30C3\u30AF\u30B9\u30FB\u30AC\u30B9\u30C8\u30FC\u75C7\u5019\u7FA4\uFF08\u30EC\u30CE\u30C3\u30AF\u30B9\u30FB\u30AC\u30B9\u30C8\u30FC\u3057\u3087\u3046\u3053\u3046\u3050\u3093\u3001Lennox\u2013Gastaut syndrome, LGS\uFF09\u3068\u306F\u3001\u5C0F\u5150\u671F\u306B\u767A\u75C7\u3059\u308B\u96E3\u6CBB\u6027\u306E\u3066\u3093\u304B\u3093\u3067\u3001\u7279\u306B2\u6B73\u304B\u30896\u6B73\u306E\u9593\u306B\u597D\u767A\u3059\u308B\u3002\u591A\u5F69\u306A\u3066\u3093\u304B\u3093\u767A\u4F5C\u304C\u983B\u7E41\u306B\u8D77\u304D\u308B\u3001\u8133\u6CE2\u691C\u67FB\u30672.5 Hz\u672A\u6E80\u306E\u9045\u3044\u304C\u691C\u51FA\u3055\u308C\u308B\u3001\u4E2D\u7B49\u5EA6\u304B\u3089\u91CD\u5EA6\u306E\u7CBE\u795E\u767A\u9054\u9045\u6EDE\u304C\u898B\u3089\u308C\u308B\u3001\u3068\u3044\u30463\u3064\u306E\u5FB4\u5019\u3092\u7279\u5FB4\u3068\u3059\u308B\u3002\u65E5\u672C\u3067\u306F\u6307\u5B9A\u96E3\u75C5144\u306B\u6307\u5B9A\u3055\u308C\u3066\u3044\u308B\u3002"@ja . . . . . . . . . . . . . . . . . . . . . . . . . "La sindrome di Lennox-Gastaut (o LGS dalla lingua inglese Lennox\u2013Gastaut syndrome) \u00E8 un'encefalopatia epilettica et\u00E0-dipendente, ad esordio infantile, caratterizzata dalla presenza di crisi polimorfe, farmacoresistenti, associate a deterioramento cognitivo e ad un EEG tipico. \u00C8 classificata come encefalopatia epilettica generalizzata (ILAE 2001)."@it . "\u30EC\u30CE\u30C3\u30AF\u30B9\u30FB\u30AC\u30B9\u30C8\u30FC\u75C7\u5019\u7FA4"@ja . . . "G40.4"@en . . . . . "250"^^ . . . "\u0645\u062A\u0644\u0627\u0632\u0645\u0629 \u0644\u064A\u0646\u0648\u0643\u0633-\u063A\u0627\u0633\u062A\u0648 (LGS) \u0647\u064A \u062D\u0627\u0644\u0629 \u0635\u0631\u0639 \u0628\u062F\u0627\u0626\u064A\u0629 \u0639\u0646\u062F \u0627\u0644\u0623\u0637\u0641\u0627\u0644 \u0648\u062A\u0638\u0647\u0631 \u063A\u0627\u0644\u0628\u0627\u064B \u0639\u0646\u062F \u0627\u0644\u0641\u0626\u0629 \u0627\u0644\u0639\u0645\u0631\u064A\u0629 \u0645\u0646 \u0633\u0646\u062A\u064A\u0646 \u0625\u0644\u0649 \u0633\u062A \u0633\u0646\u0648\u0627\u062A. \u0648\u062A\u062A\u0645\u062B\u0644 \u0628\u062B\u0644\u0627\u062B \u0639\u0644\u0627\u0645\u0627\u062A \u0645\u0646\u0647\u0627 \u0646\u0648\u0628\u0627\u062A \u0635\u0631\u0639 \u0645\u062A\u0639\u062F\u062F\u0629 \u0627\u0644\u0623\u0646\u0648\u0627\u0639 \u0645\u062A\u0643\u0631\u0631\u0629\u060C \u0646\u0645\u0637 \u063A\u064A\u0631 \u0637\u0628\u064A\u0639\u064A \u0645\u0646 \u0645\u0648\u062C\u0627\u062A \u0627\u0644\u062F\u0645\u0627\u063A \u062A\u0643\u0648\u0646 \u0639\u0628\u0627\u0631\u0629 \u0639\u0646 \u0646\u0634\u0627\u0637 \u0645\u0648\u062C\u064A \u0628\u0637\u064A\u0621 \u062A\u0631\u062F\u062F\u0647 \u0623\u0642\u0644 \u0645\u0646 2.5 \u0647\u064A\u0631\u062A\u0632\u060C \u0648\u064A\u062A\u0631\u0627\u0648\u062D \u0627\u0644\u0627\u0639\u062A\u0644\u0627\u0644 \u0627\u0644\u0639\u0642\u0644\u064A \u0641\u064A \u0647\u0630\u0647 \u0627\u0644\u062D\u0627\u0644\u0629 \u0645\u0646 \u0645\u0639\u062A\u062F\u0644 \u0625\u0644\u0649 \u062D\u0627\u062F."@ar . . "Lennox\u2013Gastaut syndrome"@en . . . . . . "El s\u00EDndrome de Lennox-Gastaut (LGS), tambi\u00E9n conocido como s\u00EDndrome de Lennox, es una variante de epilepsia infantil de dif\u00EDcil manejo, que aparece entre los dos y seis a\u00F1os de vida, y que se caracteriza por convulsiones frecuentes y diversas; a menudo se acompa\u00F1a de discapacidad intelectual y problemas conductuales. Aproximadamente el 5% de los pacientes con s\u00EDndrome de Lennox-Gastaut muere por este desorden o por los problemas asociados al mismo en unos 10 a\u00F1os desde el comienzo. A menudo, el desorden se prolonga durante la adolescencia y la edad adulta causando m\u00FAltiples problemas emocionales y discapacidades en casi todos los pacientes. Los sujetos muestran dificultades de aprendizaje, p\u00E9rdida de memoria, y alteraciones de los movimientos. El 50% de los que llegan a la edad adulta est\u00E1n totalmente discapacitados, y tan solo el 17% puede valerse por s\u00ED mismo."@es . . . "Lennox\u2013Gastaut syndrome (LGS) is a complex, rare, and severe childhood-onset epilepsy. It is characterized by multiple and concurrent seizure types, cognitive dysfunction, and slow spike waves on electroencephalogram (EEG). Typically, it presents in children aged 3\u20135 years and can persist into adulthood. It has been associated with several gene mutations, perinatal injuries, congenital infections, brain tumors/malformations, and genetic disorders such as tuberous sclerosis and West syndrome. The prognosis for LGS is poor with a 5% mortality in childhood and persistent seizures into adulthood (80%\u201390%)."@en . "Zesp\u00F3\u0142 Lennoxa-Gastauta rozwija si\u0119 mi\u0119dzy 1-8 rokiem \u017Cycia, cz\u0119\u015Bciej u ch\u0142opc\u00F3w. W sumie stanowi ok. 5-10% przypadk\u00F3w zespo\u0142\u00F3w padaczkowych u dzieci. Podobnie jak zesp\u00F3\u0142 Westa nale\u017Cy do grupy padaczek lekoopornych. Objawy zespo\u0142u s\u0105 zr\u00F3\u017Cnicowane. Mog\u0105 to by\u0107 napady atoniczne, z nag\u0142\u0105 utrat\u0105 napi\u0119cia mi\u0119\u015Bni i upadkiem, lub te\u017C napady miokloniczne ze skurczem grup mi\u0119\u015Bniowych. W zespole tym mog\u0105 si\u0119 r\u00F3wnie\u017C zdarzy\u0107 miokloniczno-astatyczne objawy b\u0119d\u0105ce po\u0142\u0105czeniem dw\u00F3ch wspomnianych wcze\u015Bniej typ\u00F3w. S\u0105 one przez to do\u015B\u0107 niebezpieczne dla zdrowia a nawet \u017Cycia dziecka, gdy\u017C towarzysz\u0105 im liczne obra\u017Cenia cia\u0142a w trakcie upadku. Ostatnim rodzajem s\u0105 nietypowe napady nie\u015Bwiadomo\u015Bci, z d\u0142u\u017Cszym okresem trwania (>20 sek.), automatyzmami, cz\u0119\u015Bciowymi utratami przytomno\u015Bci. S\u0105 one charakterystyczn"@pl . . . "\uB808\uB179\uC2A4-\uAC00\uC2A4\uD1A0 \uC99D\uD6C4\uAD70(Lennox\u2013Gastaut syndrome,LGS)\uC740 \uBCF5\uC7A1\uD558\uACE0 \uB4DC\uBB3C\uACE0 \uC2EC\uD55C \uC544\uB3D9\uAE30 \uBC1C\uC791 \uAC04\uC9C8\uC774\uB2E4. \uC774\uAC83\uC740 \uC5EC\uB7EC \uAC1C\uC758 \uB3D9\uC2DC \uBC1C\uC791 \uC720\uD615\uACFC \uC778\uC9C0 \uAE30\uB2A5 \uC7A5\uC560 \uBC0F \uB1CC\uC804\uB3C4 (EEG) \uB1CC\uD30C\uC758 \uB290\uB9B0 \uC2A4\uD30C\uC774\uD06C \uD30C\uB85C \uD2B9\uC9D5 \uC9C0\uC5B4\uC9C4\uB2E4. \uC77C\uBC18\uC801\uC73C\uB85C 3 ~ 5 \uC138 \uC5B4\uB9B0\uC774\uC5D0\uAC8C\uC11C \uBCF4\uC5EC\uC9C0\uBA70 \uC131\uC778\uC774 \uB420 \uC218 \uC788\uB2E4. \uC5EC\uB7EC \uC720\uC804\uC790 \uB3CC\uC5F0\uBCC0\uC774, \uC8FC\uC0B0\uAE30(\u5468\u7523\u671F) \uBC1C\uB2EC\uC7A5\uC560, \uC120\uCC9C\uC131 \uAC10\uC5FC, \uB1CC\uC885\uC591 / \uBCC0\uD615, (Tuberous sclerosis) \uBC0F (West Syndrome)\uACFC \uAC19\uC740 \uC720\uC804\uC801 \uC7A5\uC560\uC640 \uAD00\uB828\uC774 \uC788\uB2E4. LGS\uC5D0 \uB300\uD55C \uC608\uD6C4\uB294 \uC720\uB144\uAE30 \uC0AC\uB9DD\uB960\uC774 5 %\uC774\uACE0 \uC131\uC778\uC73C\uB85C\uC758 \uC9C0\uC18D\uC801\uC778 \uBC1C\uC791 (80 % -90 %)\uC73C\uB85C \uC88B\uC9C0 \uC54A\uC740 \uAC83\uC73C\uB85C \uC54C\uB824\uC838\uC788\uB2E4. LGS\uB294 \uC2E0\uACBD\uACFC \uC804\uBB38\uC758\uC778 \uC70C\uB9AC\uC5C4 \uB808\uB179\uC2A4(William G. Lennox)\uC640 (Henri Gastaut)\uC758 \uC774\uB984\uC744 \uB530\uB790\uB2E4. LGS\uC5D0\uB300\uD55C \uC778\uC2DD\uC744 \uC704\uD574 \uAD6D\uC81C LGS \uB0A0\uC740 11\uC6D4 1\uC77C\uB2E4."@ko . "Lennox-Gastauts syndrom \u00E4r en form av epilepsi som oftast debuterar vid 3 till 5 \u00E5rs \u00E5lder. 15 av 100 000 f\u00F6dda ber\u00E4knas f\u00E5 den. Inl\u00E4rningssv\u00E5righeter, dyslexi och dyskalkyli \u00E4r karakteristiska f\u00F6r denna sjukdom. Vissa av barnen \u00E4r normalbeg\u00E5vade, dock kan sjukdomen kopplas till utvecklingsst\u00F6rning. Fysiska symptom \u00E4r atypiska absenser och s\u00E5 kallade drop-attacker d\u00E4r patienten riskerar fallskador. Behandlingen av sj\u00E4lva sjukdomen \u00E4r antiepileptika (ofta lamotrigin, valproat och felbamat) men det beh\u00F6vs \u00E4ven m\u00E5nga psykosociala st\u00F6d\u00E5tg\u00E4rder med tanke p\u00E5 inl\u00E4rningssv\u00E5righeterna som tillst\u00E5ndet ger. Ofta beh\u00F6vs speciell skolg\u00E5ng, i vissa fall p\u00E5 s\u00E4rskola."@sv . "27762"^^ . . "345"^^ . . . . . . "Lennox-Gastaut-Syndrom"@de . "Le syndrome de Lennox-Gastaut, \u00E9galement connu sous le nom de syndrome de Lennox, est une forme d'\u00E9pilepsie infantile difficile \u00E0 traiter qui apparait le plus souvent entre l'\u00E2ge de 2 et 6 ans et qui se caract\u00E9rise par une r\u00E9gression psychomotrice ainsi que des crises fr\u00E9quentes et de types diff\u00E9rents (toniques avec chutes traumatisantes, g\u00E9n\u00E9ralis\u00E9es tonico-cloniques, des crises toniques nocturnes ou des absences atypiques)."@fr . .