"Doege\u2013Potter syndrome (DPS) is a paraneoplastic syndrome in which hypoglycemia is associated with solitary fibrous tumors. The hypoglycemia is the result of the tumors producing insulin-like growth factor 2. The syndrome was first described in 1930, by Karl Walter Doege (1867\u20131932), a German-American physician and by Roy Pilling Potter (1879\u20131968), an American radiologist, working independently; the full term Doege\u2013Potter syndrome was infrequently used until the publication of a 2000 article using the eponym."@en . "1058669053"^^ . "Das Doege-Potter-Syndrom (DPS) ist ein paraneoplastisches Syndrom, bei dem Hypoglyk\u00E4mie mit dem Vorkommen von Nicht-Langerhans-Insel-Fibromen in der Pleura assoziiert ist. Die Hypoglyk\u00E4mie ist Folge einer Produktion des Tumors von insulin\u00E4hnlichen Wachstumsfaktoren (IGF). Das Syndrom wurde 1930 unabh\u00E4ngig von und beschrieben, der Begriff wird seit 2000 verwendet. Das DPS ist ein seltenes (1976 wurden weniger als 100 F\u00E4lle beschrieben) Syndrom mit einer Malignit\u00E4tsrate von 12 bis 15 %. Tats\u00E4chlich ist der Zusammenhang von Hypoglyk\u00E4mie mit Fibromen selten; so verursachten in einer Studie aus dem Jahre 1981 lediglich vier Prozent von 360 solit\u00E4ren Pleurafibromen eine Hypoglyk\u00E4mie. Diese Tumoren sind normalerweise von gro\u00DFer Masse mit hoher Mitoserate.Die Resektion dieser Tumoren l\u00F6st normalerweise die Symptome."@de . . . "22534481"^^ . . "El s\u00EDndrome de Doege-Potter es un s\u00EDndrome paraneopl\u00E1sico\u200B en la que la hipoglucemia se relaciona con la presencia de uno o m\u00E1s tumores fibrosos pancre\u00E1ticos no de islotes en la cavidad pleural. La hipoglucemia es el resultado de dichos tumores productores del factor de crecimiento insul\u00EDnico tipo 2.\u200B"@es . . . "\u0421\u0438\u043D\u0434\u0440\u043E\u043C \u0414\u0451\u0433\u0435 \u2014 \u041F\u043E\u0442\u0442\u0435\u0440\u0430 (\u0430\u043D\u0433\u043B. Doege\u2013Potter syndrome, DPS) \u2014 \u0440\u0435\u0434\u043A\u0438\u0439 \u043F\u0430\u0440\u0430\u043D\u0435\u043E\u043F\u043B\u0430\u0441\u0442\u0438\u0447\u0435\u0441\u043A\u0438\u0439 \u0441\u0438\u043D\u0434\u0440\u043E\u043C, \u0433\u0438\u043F\u043E\u0433\u043B\u0438\u043A\u0435\u043C\u0438\u044F, \u0432\u044B\u0437\u044B\u0432\u0430\u0435\u043C\u0430\u044F \u043E\u0434\u0438\u043D\u043E\u0447\u043D\u043E\u0439 \u0444\u0438\u0431\u0440\u043E\u043C\u043E\u0439 \u043F\u043B\u0435\u0432\u0440\u044B, \u0432\u044B\u0440\u0430\u0431\u0430\u0442\u044B\u0432\u0430\u044E\u0449\u0435\u0439 \u0438\u043D\u0441\u0443\u043B\u0438\u043D\u043E\u043F\u043E\u0434\u043E\u0431\u043D\u044B\u0439 \u0444\u0430\u043A\u0442\u043E\u0440 \u0440\u043E\u0441\u0442\u0430 2. \u0421\u0438\u043D\u0434\u0440\u043E\u043C \u0431\u044B\u043B \u0432\u043F\u0435\u0440\u0432\u044B\u0435 \u043E\u043F\u0438\u0441\u0430\u043D \u0432 1930 \u0433\u043E\u0434\u0443 \u0432 \u043D\u0435\u0437\u0430\u0432\u0438\u0441\u0438\u043C\u044B\u0445 \u0440\u0430\u0431\u043E\u0442\u0430\u0445 \u041A\u0430\u0440\u043B\u0430 \u0412\u0430\u043B\u044C\u0442\u0435\u0440\u0430 \u0414\u0451\u0433\u0435 (Karl Walter Doege; 1867\u20141932) \u0438 \u0420\u043E\u044F \u041F\u0438\u043B\u043B\u0438\u043D\u0433\u0430 \u041F\u043E\u0442\u0442\u0435\u0440\u0430 (Roy Pilling Potter; 1879\u20141968); \u043D\u0430\u0437\u0432\u0430\u043D\u0438\u0435 \u0431\u044B\u043B\u043E \u043C\u0430\u043B\u043E\u0443\u043F\u043E\u0442\u0440\u0435\u0431\u0438\u043C\u044B\u043C \u0432\u043F\u043B\u043E\u0442\u044C \u0434\u043E \u043F\u043E\u044F\u0432\u043B\u0435\u043D\u0438\u044F \u0432 2000 \u0433. \u0441\u0442\u0430\u0442\u044C\u0438 \u041C\u0430\u0440\u0442\u0438\u043D\u0430 \u0427\u0435\u043C\u0431\u0435\u0440\u043B\u0435\u043D\u0430 \u0438 \u0414\u044D\u0432\u0438\u0434\u0430 \u041F. \u0422\u0430\u0433\u0433\u0430\u0440\u0442\u0430."@ru . "The structure of IGF-2, responsible for the hypoglycemia associated with Doege\u2013Potter syndrome"@en . . "La sindrome di Doege-Potter (DPS) \u00E8 una sindrome paraneoplastica in cui \u00E8 presente ipoglicemia associata a uno o pi\u00F9 fibromi nella cavit\u00E0 pleurica. L'ipoglicemia \u00E8 dovuta alla secrezione, da parte di questi fibromi, di fattore di crescita insulino-simile 2 (IGF-2)."@it . . . . . . . "Doege\u2013Potter syndrome (DPS) is a paraneoplastic syndrome in which hypoglycemia is associated with solitary fibrous tumors. The hypoglycemia is the result of the tumors producing insulin-like growth factor 2. The syndrome was first described in 1930, by Karl Walter Doege (1867\u20131932), a German-American physician and by Roy Pilling Potter (1879\u20131968), an American radiologist, working independently; the full term Doege\u2013Potter syndrome was infrequently used until the publication of a 2000 article using the eponym. DPS is rare (as of 1976, less than one hundred cases were described), with a malignancy rate of 12\u201315%. Actual rates of hypoglycemia associated with a fibrous tumor are quite rare (a 1981 study of 360 solitary fibrous tumors of the lungs found that only 4% caused hypoglycemia), and are linked to large tumors with high rates of mitosis. Removal of the tumor will normally resolve the symptoms. Tumors causing DPS tend to be quite large; in one case a 3 kg (6.6 lb), 23\u00D721\u00D712 cm (9.1\u00D78.3\u00D74.7 in) mass was removed, sufficiently large to cause a collapsed lung. In X-rays, they appear as a single mass with visible, defined borders, appearing at the edges of the lungs or a fissure dividing the lobes of the lungs. Similar hypoglycemic effects have been related to mesenchymal tumors."@en . . . . . "\u0421\u0438\u043D\u0434\u0440\u043E\u043C \u0414\u0451\u0433\u0435 \u2014 \u041F\u043E\u0442\u0442\u0435\u0440\u0430 (\u0430\u043D\u0433\u043B. Doege\u2013Potter syndrome, DPS) \u2014 \u0440\u0435\u0434\u043A\u0438\u0439 \u043F\u0430\u0440\u0430\u043D\u0435\u043E\u043F\u043B\u0430\u0441\u0442\u0438\u0447\u0435\u0441\u043A\u0438\u0439 \u0441\u0438\u043D\u0434\u0440\u043E\u043C, \u0433\u0438\u043F\u043E\u0433\u043B\u0438\u043A\u0435\u043C\u0438\u044F, \u0432\u044B\u0437\u044B\u0432\u0430\u0435\u043C\u0430\u044F \u043E\u0434\u0438\u043D\u043E\u0447\u043D\u043E\u0439 \u0444\u0438\u0431\u0440\u043E\u043C\u043E\u0439 \u043F\u043B\u0435\u0432\u0440\u044B, \u0432\u044B\u0440\u0430\u0431\u0430\u0442\u044B\u0432\u0430\u044E\u0449\u0435\u0439 \u0438\u043D\u0441\u0443\u043B\u0438\u043D\u043E\u043F\u043E\u0434\u043E\u0431\u043D\u044B\u0439 \u0444\u0430\u043A\u0442\u043E\u0440 \u0440\u043E\u0441\u0442\u0430 2. \u0421\u0438\u043D\u0434\u0440\u043E\u043C \u0431\u044B\u043B \u0432\u043F\u0435\u0440\u0432\u044B\u0435 \u043E\u043F\u0438\u0441\u0430\u043D \u0432 1930 \u0433\u043E\u0434\u0443 \u0432 \u043D\u0435\u0437\u0430\u0432\u0438\u0441\u0438\u043C\u044B\u0445 \u0440\u0430\u0431\u043E\u0442\u0430\u0445 \u041A\u0430\u0440\u043B\u0430 \u0412\u0430\u043B\u044C\u0442\u0435\u0440\u0430 \u0414\u0451\u0433\u0435 (Karl Walter Doege; 1867\u20141932) \u0438 \u0420\u043E\u044F \u041F\u0438\u043B\u043B\u0438\u043D\u0433\u0430 \u041F\u043E\u0442\u0442\u0435\u0440\u0430 (Roy Pilling Potter; 1879\u20141968); \u043D\u0430\u0437\u0432\u0430\u043D\u0438\u0435 \u0431\u044B\u043B\u043E \u043C\u0430\u043B\u043E\u0443\u043F\u043E\u0442\u0440\u0435\u0431\u0438\u043C\u044B\u043C \u0432\u043F\u043B\u043E\u0442\u044C \u0434\u043E \u043F\u043E\u044F\u0432\u043B\u0435\u043D\u0438\u044F \u0432 2000 \u0433. \u0441\u0442\u0430\u0442\u044C\u0438 \u041C\u0430\u0440\u0442\u0438\u043D\u0430 \u0427\u0435\u043C\u0431\u0435\u0440\u043B\u0435\u043D\u0430 \u0438 \u0414\u044D\u0432\u0438\u0434\u0430 \u041F. \u0422\u0430\u0433\u0433\u0430\u0440\u0442\u0430. \u0421\u0438\u043D\u0434\u0440\u043E\u043C \u0414\u0451\u0433\u0435 \u2014 \u041F\u043E\u0442\u0442\u0435\u0440\u0430 \u0432\u0441\u0442\u0440\u0435\u0447\u0430\u0435\u0442\u0441\u044F \u0432\u0435\u0441\u044C\u043C\u0430 \u0440\u0435\u0434\u043A\u043E (\u0441 1976 \u0433\u043E\u0434\u0430 \u043E\u043F\u0438\u0441\u0430\u043D\u043E \u043C\u0435\u043D\u0435\u0435 100 \u0441\u043B\u0443\u0447\u0430\u0435\u0432), \u0443\u0440\u043E\u0432\u0435\u043D\u044C \u0437\u043B\u043E\u043A\u0430\u0447\u0435\u0441\u0442\u0432\u0435\u043D\u043D\u043E\u0441\u0442\u0438 12\u201415 %. \u041F\u043E\u043A\u0430\u0437\u0430\u043D\u043E, \u0447\u0442\u043E \u043B\u0438\u0448\u044C 4 % \u0438\u0437 360 \u043E\u0431\u0441\u043B\u0435\u0434\u043E\u0432\u0430\u043D\u043D\u044B\u0445 \u0444\u0438\u0431\u0440\u043E\u043C \u043B\u0451\u0433\u043A\u043E\u0433\u043E \u0434\u0435\u0439\u0441\u0442\u0432\u0438\u0442\u0435\u043B\u044C\u043D\u043E \u0432\u044B\u0437\u044B\u0432\u0430\u043B\u0438 \u0433\u0438\u043F\u043E\u0433\u043B\u0438\u043A\u0435\u043C\u0438\u044E; \u0434\u043B\u044F \u043F\u0440\u043E\u044F\u0432\u043B\u0435\u043D\u0438\u044F \u0441\u0438\u043D\u0434\u0440\u043E\u043C\u0430 \u043D\u0435\u043E\u0431\u0445\u043E\u0434\u0438\u043C\u043E, \u0447\u0442\u043E\u0431\u044B \u043E\u043F\u0443\u0445\u043E\u043B\u044C \u0431\u044B\u043B\u0430 \u0434\u043E\u0432\u043E\u043B\u044C\u043D\u043E \u0437\u043D\u0430\u0447\u0438\u0442\u0435\u043B\u044C\u043D\u043E\u0433\u043E \u0440\u0430\u0437\u043C\u0435\u0440\u0430. \u041F\u043E\u0441\u043B\u0435 \u0443\u0434\u0430\u043B\u0435\u043D\u0438\u044F \u043E\u043F\u0443\u0445\u043E\u043B\u0438 \u0441\u0438\u043D\u0434\u0440\u043E\u043C \u0438\u0441\u0447\u0435\u0437\u0430\u0435\u0442."@ru . . . . "Das Doege-Potter-Syndrom (DPS) ist ein paraneoplastisches Syndrom, bei dem Hypoglyk\u00E4mie mit dem Vorkommen von Nicht-Langerhans-Insel-Fibromen in der Pleura assoziiert ist. Die Hypoglyk\u00E4mie ist Folge einer Produktion des Tumors von insulin\u00E4hnlichen Wachstumsfaktoren (IGF). Das Syndrom wurde 1930 unabh\u00E4ngig von und beschrieben, der Begriff wird seit 2000 verwendet. Das DPS ist ein seltenes (1976 wurden weniger als 100 F\u00E4lle beschrieben) Syndrom mit einer Malignit\u00E4tsrate von 12 bis 15 %. Tats\u00E4chlich ist der Zusammenhang von Hypoglyk\u00E4mie mit Fibromen selten; so verursachten in einer Studie aus dem Jahre 1981 lediglich vier Prozent von 360 solit\u00E4ren Pleurafibromen eine Hypoglyk\u00E4mie. Diese Tumoren sind normalerweise von gro\u00DFer Masse mit hoher Mitoserate.Die Resektion dieser Tumoren l\u00F6st normal"@de . "S\u00EDndrome de Doege-Potter"@pt . . "\u0421\u0438\u043D\u0434\u0440\u043E\u043C \u0414\u0451\u0433\u0435 \u2014 \u041F\u043E\u0442\u0442\u0435\u0440\u0430"@ru . "S\u00EDndrome de Doege-Potter"@es . . . . . . . "Doege\u2013Potter syndrome"@en . . "Syndrome de Doege-Potter"@fr . "La sindrome di Doege-Potter (DPS) \u00E8 una sindrome paraneoplastica in cui \u00E8 presente ipoglicemia associata a uno o pi\u00F9 fibromi nella cavit\u00E0 pleurica. L'ipoglicemia \u00E8 dovuta alla secrezione, da parte di questi fibromi, di fattore di crescita insulino-simile 2 (IGF-2)."@it . . . . "El s\u00EDndrome de Doege-Potter es un s\u00EDndrome paraneopl\u00E1sico\u200B en la que la hipoglucemia se relaciona con la presencia de uno o m\u00E1s tumores fibrosos pancre\u00E1ticos no de islotes en la cavidad pleural. La hipoglucemia es el resultado de dichos tumores productores del factor de crecimiento insul\u00EDnico tipo 2.\u200B Los tumores causantes del SDP tienden a ser muy grandes:\u200B en un caso fue extirpado uno de tres kilos, con un volumen de 23 cm por 21 cm por 12 cm, lo suficientemente grande para causar un colapso pulmonar.\u200B En las radiograf\u00EDas, en las que se presenta como una sola masa con bordes bien definidos visibles, aparece en los bordes de los pulmones o como una fisura que divide los l\u00F3bulos de los pulmones.\u200B Similares efectos hipoglucemiantes se han relacionado con tumores mesenquimales.\u200B"@es . . . . . . "Doege\u2013Potter syndrome"@en . "Le syndrome de Doege-Potter est un syndrome paran\u00E9oplasique caus\u00E9 par une tumeur b\u00E9nigne ou maligne, le plus souvent une tumeur fibreuse solitaire."@fr . . . . . . . . . . . . . "Sindrome di Doege-Potter"@it . . . . . . . . . "Doege-Potter-Syndrom"@de . . "A s\u00EDndrome de Doege-Potter \u00E9 uma s\u00EDndrome paraneopl\u00E1sica onde a hipoglicemia est\u00E1 relacionada com o aparecimento de tumores em ilhotas n\u00E3o fibrosas da cavidade pleural. A hipoclicemia resulta da produ\u00E7\u00E3o de IGF-2 pelos tumores. Tem baixa taxa de malignidade, sendo descrita por Doege e Potter em 1930. O tratamento consiste na retirada dos tumores. Trata-se de um transtorno raro, havendo menos de cem casos relatados em 1976. \u00C9 mais comum entre a sexta e a s\u00E9tima d\u00E9cada de vida, afetando ambos os sexos igualmente."@pt . "Le syndrome de Doege-Potter est un syndrome paran\u00E9oplasique caus\u00E9 par une tumeur b\u00E9nigne ou maligne, le plus souvent une tumeur fibreuse solitaire."@fr . . "5524"^^ . . "A s\u00EDndrome de Doege-Potter \u00E9 uma s\u00EDndrome paraneopl\u00E1sica onde a hipoglicemia est\u00E1 relacionada com o aparecimento de tumores em ilhotas n\u00E3o fibrosas da cavidade pleural. A hipoclicemia resulta da produ\u00E7\u00E3o de IGF-2 pelos tumores. Tem baixa taxa de malignidade, sendo descrita por Doege e Potter em 1930. O tratamento consiste na retirada dos tumores. Trata-se de um transtorno raro, havendo menos de cem casos relatados em 1976. \u00C9 mais comum entre a sexta e a s\u00E9tima d\u00E9cada de vida, afetando ambos os sexos igualmente."@pt .