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Statements

Subject Item
dbr:Multifocal_fibrosclerosis
rdf:type
dbo:Disease wikidata:Q12136 owl:Thing
rdfs:label
Multifocal fibrosclerosis
rdfs:comment
Multifocal fibrosclerosis and idiopathic fibrosclerosis are disorders of unknown aetiology, characterised by fibrous lesions (co-)occurring at a variety of sites. Known manifestations include retroperitoneal fibrosis, mediastinal fibrosis and Riedel's thyroiditis. They are now considered to be manifestations of IgG4-related disease.
foaf:name
Multifocal fibrosclerosis
dbp:name
Multifocal fibrosclerosis
foaf:depiction
n13:Autosomal_recessive_-_en.svg
dct:subject
dbc:Idiopathic_diseases dbc:IgG4-related_disease
dbo:wikiPageID
24793458
dbo:wikiPageRevisionID
1014188777
dbo:wikiPageWikiLink
dbr:Lesion dbr:Retroperitoneal_fibrosis dbc:Idiopathic_diseases dbr:Riedel's_thyroiditis dbr:IgG4-related_disease dbr:Mediastinal_fibrosis dbc:IgG4-related_disease
owl:sameAs
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n13:Autosomal_recessive_-_en.svg?width=300
dbp:icd
N13.5
dbp:omim
228800
dbp:orphanet
49041
dbp:caption
Multifocal fibrosclerosis is inherited in an autosomal recessive manner
dbp:synonyms
Idiopathic fibrosclerosis
dbo:abstract
Multifocal fibrosclerosis and idiopathic fibrosclerosis are disorders of unknown aetiology, characterised by fibrous lesions (co-)occurring at a variety of sites. Known manifestations include retroperitoneal fibrosis, mediastinal fibrosis and Riedel's thyroiditis. They are now considered to be manifestations of IgG4-related disease.
dbp:mesh
D012185
gold:hypernym
dbr:Disorders
prov:wasDerivedFrom
wikipedia-en:Multifocal_fibrosclerosis?oldid=1014188777&ns=0
dbo:wikiPageLength
2718
dbo:icd10
N13.5
dbo:omim
228800
dbo:orpha
49041
foaf:isPrimaryTopicOf
wikipedia-en:Multifocal_fibrosclerosis