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Doege–Potter syndrome (DPS) is a paraneoplastic syndrome in which hypoglycemia is associated with solitary fibrous tumors. The hypoglycemia is the result of the tumors producing insulin-like growth factor 2. The syndrome was first described in 1930, by Karl Walter Doege (1867–1932), a German-American physician and by Roy Pilling Potter (1879–1968), an American radiologist, working independently; the full term Doege–Potter syndrome was infrequently used until the publication of a 2000 article using the eponym.

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  • Doege-Potter-Syndrom
  • Doege–Potter syndrome
  • Síndrome de Doege-Potter
  • Syndrome de Doege-Potter
  • Sindrome di Doege-Potter
  • Síndrome de Doege-Potter
  • Синдром Дёге — Поттера
rdfs:comment
  • Le Syndrome de Doege-Potter est un syndrome paranéoplasique causé par une tumeur bénigne ou maligne, le plus souvent une tumeur fibreuse solitaire.
  • La sindrome di Doege-Potter (DPS) è una sindrome paraneoplastica in cui è presente ipoglicemia associata a uno o più fibromi nella cavità pleurica. L'ipoglicemia è dovuta alla secrezione, da parte di questi fibromi, di fattore di crescita insulino-simile 2 (IGF-2).
  • A síndrome de Doege-Potter é uma síndrome paraneoplásica onde a hipoglicemia está relacionada com o aparecimento de tumores em ilhotas não fibrosas da cavidade pleural. A hipoclicemia resulta da produção de IGF-II pelos tumores. Tem baixa taxa de malignidade, sendo descrita por Doege e Potter em 1930. O tratamento consiste na retirada dos tumores. Trata-se de um transtorno raro, havendo menos de 100 casos relatados desde 1976. É mais comum entre a sexta e a sétima década de vida, afetando ambos os sexos igualmente.
  • Das Doege-Potter-Syndrom (DPS) ist ein paraneoplastisches Syndrom, bei dem Hypoglykämie mit dem Vorkommen von Nicht-Langerhans-Insel-Fibromen in der Pleura assoziiert ist. Die Hypoglykämie ist Folge einer Produktion des Tumors von insulinähnlichen Wachstumsfaktoren (IGF). Das Syndrom wurde 1930 unabhängig von und beschrieben, der Begriff wird seit 2000 verwendet. Das DPS ist ein seltenes (1976 wurden weniger als 100 Fälle beschrieben) Syndrom mit einer Malignitätsrate von 12 bis 15 %. Tatsächlich ist der Zusammenhang von Hypoglykämie mit Fibromen selten; so verursachten in einer Studie aus dem Jahre 1981 lediglich vier Prozent von 360 solitären Pleurafibromen eine Hypoglykämie. Diese Tumoren sind normalerweise von großer Masse mit hoher Mitoserate.Die Resektion dieser Tumoren löst normal
  • El síndrome de Doege-Potter es un síndrome paraneoplásico​ en la que la hipoglucemia se relaciona con la presencia de uno o más tumores fibrosos pancreáticos no de islotes en la cavidad pleural. La hipoglucemia es el resultado de dichos tumores productores del factor de crecimiento insulínico tipo 2.​
  • Doege–Potter syndrome (DPS) is a paraneoplastic syndrome in which hypoglycemia is associated with solitary fibrous tumors. The hypoglycemia is the result of the tumors producing insulin-like growth factor 2. The syndrome was first described in 1930, by Karl Walter Doege (1867–1932), a German-American physician and by Roy Pilling Potter (1879–1968), an American radiologist, working independently; the full term Doege–Potter syndrome was infrequently used until the publication of a 2000 article using the eponym.
  • Синдром Дёге — Поттера (англ. Doege–Potter syndrome, DPS) — редкий паранеопластический синдром, гипогликемия, вызываемая одиночной фибромой плевры, вырабатывающей инсулиноподобный фактор роста 2. Синдром был впервые описан в 1930 году в независимых работах Карла Вальтера Дёге (Karl Walter Doege; 1867—1932) и Роя Пиллинга Поттера (Roy Pilling Potter; 1879—1968); название было малоупотребимым вплоть до появления в 2000 г. статьи Мартина Чемберлена и Дэвида П. Таггарта.
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  • Doege–Potter syndrome
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  • Doege–Potter syndrome
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  • The structure of IGF-2, responsible for the hypoglycemia associated with Doege–Potter syndrome
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  • El síndrome de Doege-Potter es un síndrome paraneoplásico​ en la que la hipoglucemia se relaciona con la presencia de uno o más tumores fibrosos pancreáticos no de islotes en la cavidad pleural. La hipoglucemia es el resultado de dichos tumores productores del factor de crecimiento insulínico tipo 2.​ Los tumores causantes del SDP tienden a ser muy grandes:​ en un caso fue extirpado uno de tres kilos, con un volumen de 23 cm por 21 cm por 12 cm, lo suficientemente grande para causar un colapso pulmonar.​ En las radiografías, en las que se presenta como una sola masa con bordes bien definidos visibles, aparece en los bordes de los pulmones o como una fisura que divide los lóbulos de los pulmones.​ Similares efectos hipoglucemiantes se han relacionado con tumores mesenquimales.​
  • Das Doege-Potter-Syndrom (DPS) ist ein paraneoplastisches Syndrom, bei dem Hypoglykämie mit dem Vorkommen von Nicht-Langerhans-Insel-Fibromen in der Pleura assoziiert ist. Die Hypoglykämie ist Folge einer Produktion des Tumors von insulinähnlichen Wachstumsfaktoren (IGF). Das Syndrom wurde 1930 unabhängig von und beschrieben, der Begriff wird seit 2000 verwendet. Das DPS ist ein seltenes (1976 wurden weniger als 100 Fälle beschrieben) Syndrom mit einer Malignitätsrate von 12 bis 15 %. Tatsächlich ist der Zusammenhang von Hypoglykämie mit Fibromen selten; so verursachten in einer Studie aus dem Jahre 1981 lediglich vier Prozent von 360 solitären Pleurafibromen eine Hypoglykämie. Diese Tumoren sind normalerweise von großer Masse mit hoher Mitoserate.Die Resektion dieser Tumoren löst normalerweise die Symptome.
  • Le Syndrome de Doege-Potter est un syndrome paranéoplasique causé par une tumeur bénigne ou maligne, le plus souvent une tumeur fibreuse solitaire.
  • La sindrome di Doege-Potter (DPS) è una sindrome paraneoplastica in cui è presente ipoglicemia associata a uno o più fibromi nella cavità pleurica. L'ipoglicemia è dovuta alla secrezione, da parte di questi fibromi, di fattore di crescita insulino-simile 2 (IGF-2).
  • Doege–Potter syndrome (DPS) is a paraneoplastic syndrome in which hypoglycemia is associated with solitary fibrous tumors. The hypoglycemia is the result of the tumors producing insulin-like growth factor 2. The syndrome was first described in 1930, by Karl Walter Doege (1867–1932), a German-American physician and by Roy Pilling Potter (1879–1968), an American radiologist, working independently; the full term Doege–Potter syndrome was infrequently used until the publication of a 2000 article using the eponym. DPS is rare (as of 1976, less than one hundred cases were described), with a malignancy rate of 12–15%. Actual rates of hypoglycemia associated with a fibrous tumor are quite rare (a 1981 study of 360 solitary fibrous tumors of the lungs found that only 4% caused hypoglycemia), and are linked to large tumors with high rates of mitosis. Removal of the tumor will normally resolve the symptoms. Tumors causing DPS tend to be quite large; in one case a 3 kg (6.6 lb), 23×21×12 cm (9.1×8.3×4.7 in) mass was removed, sufficiently large to cause a collapsed lung. In X-rays, they appear as a single mass with visible, defined borders, appearing at the edges of the lungs or a fissure dividing the lobes of the lungs. Similar hypoglycemic effects have been related to mesenchymal tumors.
  • A síndrome de Doege-Potter é uma síndrome paraneoplásica onde a hipoglicemia está relacionada com o aparecimento de tumores em ilhotas não fibrosas da cavidade pleural. A hipoclicemia resulta da produção de IGF-II pelos tumores. Tem baixa taxa de malignidade, sendo descrita por Doege e Potter em 1930. O tratamento consiste na retirada dos tumores. Trata-se de um transtorno raro, havendo menos de 100 casos relatados desde 1976. É mais comum entre a sexta e a sétima década de vida, afetando ambos os sexos igualmente.
  • Синдром Дёге — Поттера (англ. Doege–Potter syndrome, DPS) — редкий паранеопластический синдром, гипогликемия, вызываемая одиночной фибромой плевры, вырабатывающей инсулиноподобный фактор роста 2. Синдром был впервые описан в 1930 году в независимых работах Карла Вальтера Дёге (Karl Walter Doege; 1867—1932) и Роя Пиллинга Поттера (Roy Pilling Potter; 1879—1968); название было малоупотребимым вплоть до появления в 2000 г. статьи Мартина Чемберлена и Дэвида П. Таггарта. Синдром Дёге — Поттера встречается весьма редко (с 1976 года описано менее 100 случаев), уровень злокачественности 12-15 %. Показано, что лишь 4 % из 360 обследованных фибром лёгкого действительно вызывали гипогликемию; для проявления синдрома необходимо, чтобы опухоль была довольно значительного размера. После удаления опухоли синдром исчезает.
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