Scleromyositis, is an autoimmune disease (a disease in which the immune system attacks the body). People with scleromyositis have symptoms of both systemic scleroderma and either polymyositis or dermatomyositis, and is therefore considered an overlap syndrome. Although it is a rare disease, it is one of the more common overlap syndromes seen in scleroderma patients, together with MCTD and Antisynthetase syndrome. Autoantibodies often found in these patients are the anti-PM/Scl (anti-exosome) antibodies.
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| - التهاب العضل التصلبي (ar)
- Escleromiositis (ca)
- Scleromiosite (it)
- Scleromyositis (en)
- Escleromiosite (pt)
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| - التهاب العضل التصلبي (Scleromyositis) أو PM/Scl overlap syndrome هي داء مناعة ذاتية معقد (مرض يقوم فيه جهاز المناعة بمهاجمة الجسم). المرضى المصابين بالتهاب العضل التصلبي يعانون من أعراض تصلب الجلد المجموعي وإما التهاب العضلات أو التهاب الجلد والعضل، وبالتالي تُعتبر متلازمة متراكبة. وعلى الرغم من أنها تُعتبر مرضًا نادرًا، إلا أنها واحدة من المتلازمات المتراكبة الأكثر شيوعًا التي تُلاحظ في مرضى تصلب الجلد جنبًا إلى جنب مع داء النسيج الضام المختلط والمتلازمة المخلقة. الأجسام المضادة الذاتية التي توجد في كثير من الأحيان لدى المرضى هي anti-PM/Scl anti-exosome. (ar)
- L'escleromiositis o síndrome de superposició PM/Scl és una malaltia autoimmunitària. Tot i ser una malaltia poc freqüent, és una de les síndromes de superposició més comunes vistes en pacients amb esclerodèrmia, juntament amb la (MCTD, de l'anglès mixed connective tissue disease) i la . Els autoanticossos d'aquests pacients sovint són els anti-PM/Scl (anti-exosome). (ca)
- Scleromyositis, is an autoimmune disease (a disease in which the immune system attacks the body). People with scleromyositis have symptoms of both systemic scleroderma and either polymyositis or dermatomyositis, and is therefore considered an overlap syndrome. Although it is a rare disease, it is one of the more common overlap syndromes seen in scleroderma patients, together with MCTD and Antisynthetase syndrome. Autoantibodies often found in these patients are the anti-PM/Scl (anti-exosome) antibodies. (en)
- La scleromiosite è una malattia autoimmune (una malattia in cui il sistema immunitario attacca il corpo). Le persone con scleromiosite hanno sintomi sia di sclerodermia sistemica sia di polimiosite o dermatomiosite, ed è quindi considerata una . Sebbene sia una malattia rara, è una delle sindromi da sovrapposizione più comuni osservate nei pazienti con sclerodermia, insieme alla MCTD e alla . Gli autoanticorpi che si trovano spesso in questi pazienti sono gli anticorpi anti-PM/Scl (anti- esosoma). (it)
- A escleromiosite ou síndrome de sobreposição de PM/Scl é uma . Apesar de ser uma doença rara, é uma das síndromes de sobreposição mais comuns observadas em pacientes com esclerodermia, juntamente com a e a . Os autoanticorpos frequentemente encontrados nestes pacientes são os anti-PM/Scl (anti-exossomo). (pt)
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| - PM/Scl overlap syndrome (en)
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| - L'escleromiositis o síndrome de superposició PM/Scl és una malaltia autoimmunitària. Tot i ser una malaltia poc freqüent, és una de les síndromes de superposició més comunes vistes en pacients amb esclerodèrmia, juntament amb la (MCTD, de l'anglès mixed connective tissue disease) i la . Els autoanticossos d'aquests pacients sovint són els anti-PM/Scl (anti-exosome). Els símptomes que s'observen amb major freqüència són símptomes típics de la persona i de les malalties autoimmunitàries: el fenomen de Raynaud, artritis, miositis i esclerodèrmia. El tractament d'aquests pacients és similar al tractament per a malalties autoimmunitàries individuals, ja sigui immunosupressors o fàrmacs immunomoduladors. (ca)
- التهاب العضل التصلبي (Scleromyositis) أو PM/Scl overlap syndrome هي داء مناعة ذاتية معقد (مرض يقوم فيه جهاز المناعة بمهاجمة الجسم). المرضى المصابين بالتهاب العضل التصلبي يعانون من أعراض تصلب الجلد المجموعي وإما التهاب العضلات أو التهاب الجلد والعضل، وبالتالي تُعتبر متلازمة متراكبة. وعلى الرغم من أنها تُعتبر مرضًا نادرًا، إلا أنها واحدة من المتلازمات المتراكبة الأكثر شيوعًا التي تُلاحظ في مرضى تصلب الجلد جنبًا إلى جنب مع داء النسيج الضام المختلط والمتلازمة المخلقة. الأجسام المضادة الذاتية التي توجد في كثير من الأحيان لدى المرضى هي anti-PM/Scl anti-exosome. والأعراض التي تُلاحظ في معظم الأحيان هي أعراض مشابهة لأعراض أمراض المناعة الذاتية وتتضمن ظاهرة رينو والتهاب المفاصل والتهاب العضل وتصلب الجلد. وبالتالي فإن علاج هؤلاء المرضى يتوقف بشكل كبير على الأعراض الدقيقة التي يبلغها المريض للطبيب ويشبه علاج مرض المناعة الذاتية وينطوي في كثير من الأحيان على عقاقير المثبطة للمناعة أو العقاقير القادرة على تغيير طبيعة المناعة. (ar)
- Scleromyositis, is an autoimmune disease (a disease in which the immune system attacks the body). People with scleromyositis have symptoms of both systemic scleroderma and either polymyositis or dermatomyositis, and is therefore considered an overlap syndrome. Although it is a rare disease, it is one of the more common overlap syndromes seen in scleroderma patients, together with MCTD and Antisynthetase syndrome. Autoantibodies often found in these patients are the anti-PM/Scl (anti-exosome) antibodies. The symptoms that are seen most often are typical symptoms of the individual autoimmune diseases and include Raynaud's phenomenon, arthritis, myositis and scleroderma. Treatment of these patients is therefore strongly dependent on the exact symptoms with which a patient reports to a physician and is similar to treatment for the individual autoimmune disease, often involving either immunosuppressive or immunomodulating drugs. (en)
- La scleromiosite è una malattia autoimmune (una malattia in cui il sistema immunitario attacca il corpo). Le persone con scleromiosite hanno sintomi sia di sclerodermia sistemica sia di polimiosite o dermatomiosite, ed è quindi considerata una . Sebbene sia una malattia rara, è una delle sindromi da sovrapposizione più comuni osservate nei pazienti con sclerodermia, insieme alla MCTD e alla . Gli autoanticorpi che si trovano spesso in questi pazienti sono gli anticorpi anti-PM/Scl (anti- esosoma). I sintomi che si manifestano più spesso sono sintomi tipici delle singole malattie autoimmuni e comprendono il fenomeno di Raynaud, l'artrite, la miosite e la sclerodermia. Il trattamento di questi pazienti è quindi fortemente dipendente dai sintomi esatti con cui un paziente si presenta ed è simile al trattamento per la singola malattia autoimmune, che spesso coinvolge farmaci immunosoppressori o immunomodulanti. (it)
- A escleromiosite ou síndrome de sobreposição de PM/Scl é uma . Apesar de ser uma doença rara, é uma das síndromes de sobreposição mais comuns observadas em pacientes com esclerodermia, juntamente com a e a . Os autoanticorpos frequentemente encontrados nestes pacientes são os anti-PM/Scl (anti-exossomo). Os simptomas que se observam com maior frequência são sintomas típicos de doenças autoimunitárias individuais: o fenómeno de Raynaud, artrite, miosite e esclerodermia. O tratamento destes pacientes está, portanto, em grande medida dependente da exactidão do relatório médico dos sintomas do paciente e é semelhante ao tratamento de doenças autoimunitárias individuais que, amiúde, envolve quer quer drogas imunomoduladoras. (pt)
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