"La coproporfirinogeno ossidasi \u00E8 un enzima appartenente alla classe delle ossidoreduttasi, che catalizza la seguente reazione: copro III + O2 + 2 H+ \u21C4 protoporfirinogeno-IX + 2 CO2 + 2 H2O"@it . . . . "Coproporphyrinogen-Oxidase (CPOX) ist das Enzym, das die Oxidation von zu Protoporphyrinogen IX katalysiert, eine Teilreaktion bei der Biosynthese der Porphyrine, die in allen Lebewesen stattfindet. In Eukaryoten wird vorher das Substrat aus dem Zytosol in den Raum zwischen der inneren und \u00E4u\u00DFeren Membran der Mitochondrien transportiert, der beteiligte Transporter ist noch unbekannt. Beim Menschen k\u00F6nnen Mutationen am CPOX-Gen zu CPOX-Mangel und damit zu heredit\u00E4rer Koproporphyrie f\u00FChren."@de . . "\u30B3\u30D7\u30ED\u30DD\u30EB\u30D5\u30A3\u30EA\u30CE\u30FC\u30B2\u30F3\u30AA\u30AD\u30B7\u30C0\u30FC\u30BC"@ja . "Coprogen_oxidas"@en . "Coproporphyrinogen-III oxidase, mitochondrial (abbreviated as CPOX) is an enzyme that in humans is encoded by the CPOX gene. A genetic defect in the enzyme results in a reduced production of heme in animals. The medical condition associated with this enzyme defect is called hereditary coproporphyria. CPOX, the sixth enzyme of the haem biosynthetic pathway, converts coproporphyrinogen III to protoporphyrinogen IX through two sequential steps of oxidative decarboxylation. The activity of the CPOX enzyme, located in the mitochondrial membrane, is measured in lymphocytes."@en . "Coproporphyrinogen-Oxidase"@de . . . . . . . . . . "coproporphyrinogen iii oxidase from leishmania major"@en . . . . . . . . . . . . . . "PF01218"@en . . . . . "5758407"^^ . "Coproporphyrinogen III oxidase"@en . "PDOC00783"@en . . . . . . . . . . . . . "IPR001260"@en . . . . . . . . "Coproporphyrinogen-III oxidase, mitochondrial (abbreviated as CPOX) is an enzyme that in humans is encoded by the CPOX gene. A genetic defect in the enzyme results in a reduced production of heme in animals. The medical condition associated with this enzyme defect is called hereditary coproporphyria. CPOX, the sixth enzyme of the haem biosynthetic pathway, converts coproporphyrinogen III to protoporphyrinogen IX through two sequential steps of oxidative decarboxylation. The activity of the CPOX enzyme, located in the mitochondrial membrane, is measured in lymphocytes."@en . . . . . . . . . . . . . "18287"^^ . . . . "Coprogen_oxidas"@en . . . . . . "\u30B3\u30D7\u30ED\u30DD\u30EB\u30D5\u30A3\u30EA\u30CE\u30FC\u30B2\u30F3\u30AA\u30AD\u30B7\u30C0\u30FC\u30BC\uFF08coproporphyrinogen oxidase\uFF09\u306F\u3001\u30D2\u30C8\u306ECPOX\u907A\u4F1D\u5B50\u306B\u30B3\u30FC\u30C9\u3055\u308C\u3066\u3044\u308B\u9175\u7D20\u3067\u3042\u308B\u3002\u3053\u306E\u9175\u7D20\u306F\u30DD\u30EB\u30D5\u30A3\u30EA\u30F3\u4EE3\u8B1D\u306E6\u756A\u76EE\u306E\u53CD\u5FDC\u306B\u95A2\u4E0E\u3057\u3001\u30B3\u30D7\u30ED\u30DD\u30EB\u30D5\u30A3\u30EA\u30CE\u30FC\u30B2\u30F3III\u3092\u30D7\u30ED\u30C8\u30DD\u30EB\u30D5\u30A3\u30EA\u30CE\u30FC\u30B2\u30F3IX\u306B\u5909\u63DB\u3059\u308B\u3002 \n* \u30B3\u30D7\u30ED\u30DD\u30EB\u30D5\u30A3\u30EA\u30CE\u30FC\u30B2\u30F3III \n* \u30D7\u30ED\u30C8\u30DD\u30EB\u30D5\u30A3\u30EA\u30CE\u30FC\u30B2\u30F3IX"@ja . "Coproporfirinogeno ossidasi"@it . . . "Coproporphyrinogen-Oxidase (CPOX) ist das Enzym, das die Oxidation von zu Protoporphyrinogen IX katalysiert, eine Teilreaktion bei der Biosynthese der Porphyrine, die in allen Lebewesen stattfindet. In Eukaryoten wird vorher das Substrat aus dem Zytosol in den Raum zwischen der inneren und \u00E4u\u00DFeren Membran der Mitochondrien transportiert, der beteiligte Transporter ist noch unbekannt. Beim Menschen k\u00F6nnen Mutationen am CPOX-Gen zu CPOX-Mangel und damit zu heredit\u00E4rer Koproporphyrie f\u00FChren."@de . "\u30B3\u30D7\u30ED\u30DD\u30EB\u30D5\u30A3\u30EA\u30CE\u30FC\u30B2\u30F3\u30AA\u30AD\u30B7\u30C0\u30FC\u30BC\uFF08coproporphyrinogen oxidase\uFF09\u306F\u3001\u30D2\u30C8\u306ECPOX\u907A\u4F1D\u5B50\u306B\u30B3\u30FC\u30C9\u3055\u308C\u3066\u3044\u308B\u9175\u7D20\u3067\u3042\u308B\u3002\u3053\u306E\u9175\u7D20\u306F\u30DD\u30EB\u30D5\u30A3\u30EA\u30F3\u4EE3\u8B1D\u306E6\u756A\u76EE\u306E\u53CD\u5FDC\u306B\u95A2\u4E0E\u3057\u3001\u30B3\u30D7\u30ED\u30DD\u30EB\u30D5\u30A3\u30EA\u30CE\u30FC\u30B2\u30F3III\u3092\u30D7\u30ED\u30C8\u30DD\u30EB\u30D5\u30A3\u30EA\u30CE\u30FC\u30B2\u30F3IX\u306B\u5909\u63DB\u3059\u308B\u3002 \n* \u30B3\u30D7\u30ED\u30DD\u30EB\u30D5\u30A3\u30EA\u30CE\u30FC\u30B2\u30F3III \n* \u30D7\u30ED\u30C8\u30DD\u30EB\u30D5\u30A3\u30EA\u30CE\u30FC\u30B2\u30F3IX"@ja . . . . . . "1116082430"^^ . . . . . . . "La coproporfirinogeno ossidasi \u00E8 un enzima appartenente alla classe delle ossidoreduttasi, che catalizza la seguente reazione: copro III + O2 + 2 H+ \u21C4 protoporfirinogeno-IX + 2 CO2 + 2 H2O"@it . . .