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Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency is a rare autosomal recessive fatty acid oxidation disorder that prevents the body from converting certain fats into energy. This can become life-threatening, particularly during periods of fasting.

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  • Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency is a rare autosomal recessive fatty acid oxidation disorder that prevents the body from converting certain fats into energy. This can become life-threatening, particularly during periods of fasting. (en)
  • Le déficit en 3-hydroxyacyl-coenzyme A déshydrogénase des acides gras à chaîne longue, souvent abrégé en déficit en LCHAD, est l'une des maladies rares à transmission autosomique récessive lié à l'oxydation des acides gras qui empêche le corps de convertir certaines graisses en énergie. Cela peut être dangereux, en particulier pendant les périodes de jeûne. (fr)
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  • Long-chain 3-hydroxyacyl-coenzyme; A dehydrogenase deficiency has an autosomal recessive pattern of inheritance. (en)
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  • Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency (en)
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  • LCHAD deficiency (en)
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  • Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency is a rare autosomal recessive fatty acid oxidation disorder that prevents the body from converting certain fats into energy. This can become life-threatening, particularly during periods of fasting. (en)
  • Le déficit en 3-hydroxyacyl-coenzyme A déshydrogénase des acides gras à chaîne longue, souvent abrégé en déficit en LCHAD, est l'une des maladies rares à transmission autosomique récessive lié à l'oxydation des acides gras qui empêche le corps de convertir certaines graisses en énergie. Cela peut être dangereux, en particulier pendant les périodes de jeûne. (fr)
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  • Déficit en 3-hydroxyacyl-coenzyme A déshydrogénase des acides gras à chaîne longue (fr)
  • Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency (en)
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  • Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency (en)
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