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Prion disease characterized by adult onset of memory loss, dementia, ataxia, and pathologic deposition of amyloid-like plaques in the brain

Property Value
dbo:description
  • Krankheit (de)
  • betegség (hu)
  • yetişkinlikte başlayan hafıza kaybı, bunama, ataksi ve beyinde amiloid benzeri plakların patolojik birikimi ile karakterize prion hastalığı (tr)
  • Gizakietan agertzen den entzefalopatia espongiformearen aldaeretako bat. Eragin eskasa du, 100 milioi biztanleko kasu bat. Sintoma nagusiak eskuetako atzamarretako agnosia, eskuina eta ezkerra bereizteko ezintasuna, disgrafia eta akalkulia dira (eu)
  • одна з пріонових хвороб людини (uk)
  • prionska bolezen, za katero so značilni izguba spomina, demenca, ataksija in patološko odlaganje amiloidu podobnih plakov v možganih pri odraslih (sl)
  • malattia neurodegenerativa molto rara (it)
  • prion disease characterized by adult onset of memory loss, dementia, ataxia, and pathologic deposition of amyloid-like plaques in the brain (en)
  • прионное нейродегенеративное заболевание (ru)
  • forme particulière et très rare d'encéphalopathie spongiforme transmissible humaine (fr)
  • 中枢神経の遺伝性疾患 (ja)
dbo:diseasesDB
  • 30729
dbo:icd10
  • A81.9
dbo:icd9
  • 046.71
dbo:meshId
  • D016098
dbo:omim
  • 137440 (xsd:integer)
dbo:thumbnail
dbo:wikiPageExternalLink
dbo:wikiPageWikiLink
dbp:caption
  • A person with inherited prion disease has cerebellar atrophy. This is quite typical of GSS. (en)
dbp:causes
dbp:date
  • 2013-05-11 (xsd:date)
dbp:diseasesdb
  • 30729 (xsd:integer)
dbp:frequency
  • 1 (xsd:integer)
dbp:icd
  • 46.710000 (xsd:double)
  • (en)
  • A81.9 (en)
dbp:medication
  • None (en)
dbp:meshid
  • D016098 (en)
dbp:name
  • Gerstmann–Sträussler–Scheinker syndrome (en)
dbp:omim
  • 137440 (xsd:integer)
dbp:prognosis
  • -1.893456E8 (dbd:second)
dbp:symptoms
  • difficulty speaking, developing dementia, memory loss, vision loss. (en)
dbp:treatment
  • None (en)
dbp:url
dbp:wikiPageUsesTemplate
dct:subject
rdf:type
rdfs:label
  • Gerstmann–Sträussler–Scheinker syndrome (en)
  • داء غيرستمان-ستراوس (ar)
  • Síndrome de Gerstmann-Sträussler-Scheinker (ca)
  • Gerstmann-Sträussler-Scheinker-Syndrom (de)
  • Sindromo de Gerstmann-Sträussler-Scheinker (eo)
  • Síndrome de Gerstmann-Sträussler-Scheinker (es)
  • Syndrome de Gerstmann-Sträussler-Scheinker (fr)
  • ゲルストマン・ストロイスラー・シャインカー症候群 (ja)
  • Malattia di Gerstmann-Sträussler-Scheinker (it)
  • 게르스트만-슈트로이슬러-샤인커병 (ko)
  • Syndroom van Gerstmann-Sträussler-Scheinker (nl)
  • Zespół Gerstmanna-Sträusslera-Scheinkera (pl)
  • Síndrome de Gerstmann-Sträussler-Scheinker (pt)
  • Синдром Герстмана — Штраусслера — Шейнкера (ru)
  • Синдром Герстмана — Штройслера — Шейнкера (uk)
  • 格斯特曼–斯特劳斯勒–申克综合征 (zh)
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