"Famili\u00E4res Mittelmeerfieber"@de . . . . "Familj\u00E4r medelhavsfeber"@sv . "La febbre mediterranea familiare o polisierosite parossistica familiare \u00E8 una malattia genetica a trasmissione autosomica recessiva, caratterizzata da febbre ricorrente associata a peritonite o pleurite, pi\u00F9 frequente tra le popolazioni originarie del mar Mediterraneo."@it . "Famili\u00E1rn\u00ED st\u0159edomo\u0159sk\u00E1 hore\u010Dka"@cs . "249100"^^ . "1410"@en . . "'\u041F\u0435\u0440\u0438\u043E\u0434\u0438\u0447\u0435\u0441\u043A\u0430\u044F \u0431\u043E\u043B\u0435\u0437\u043D\u044C \u00A0\u2014 \u0441\u0440\u0430\u0432\u043D\u0438\u0442\u0435\u043B\u044C\u043D\u043E \u0440\u0435\u0434\u043A\u043E\u0435 \u0433\u0435\u043D\u0435\u0442\u0438\u0447\u0435\u0441\u043A\u0438 \u043E\u0431\u0443\u0441\u043B\u043E\u0432\u043B\u0435\u043D\u043D\u043E\u0435 \u043D\u0430\u0441\u043B\u0435\u0434\u0441\u0442\u0432\u0435\u043D\u043D\u043E\u0435 \u0437\u0430\u0431\u043E\u043B\u0435\u0432\u0430\u043D\u0438\u0435, \u043F\u0440\u043E\u044F\u0432\u043B\u044F\u044E\u0449\u0435\u0435\u0441\u044F \u043F\u0435\u0440\u0438\u043E\u0434\u0438\u0447\u0435\u0441\u043A\u0438 \u0440\u0435\u0446\u0438\u0434\u0438\u0432\u0438\u0440\u0443\u044E\u0449\u0438\u043C \u0441\u0435\u0440\u043E\u0437\u0438\u0442\u043E\u043C \u0438 \u043E\u0442\u043D\u043E\u0441\u0438\u0442\u0435\u043B\u044C\u043D\u043E \u0447\u0430\u0441\u0442\u044B\u043C \u0440\u0430\u0437\u0432\u0438\u0442\u0438\u0435\u043C \u0430\u043C\u0438\u043B\u043E\u0438\u0434\u043E\u0437\u0430. \u0412\u0441\u0442\u0440\u0435\u0447\u0430\u0435\u0442\u0441\u044F \u043F\u0440\u0435\u0438\u043C\u0443\u0449\u0435\u0441\u0442\u0432\u0435\u043D\u043D\u043E \u0443 \u043F\u0440\u0435\u0434\u0441\u0442\u0430\u0432\u0438\u0442\u0435\u043B\u0435\u0439 \u043D\u0430\u0440\u043E\u0434\u043D\u043E\u0441\u0442\u0435\u0439, \u043F\u0440\u0435\u0434\u043A\u0438 \u043A\u043E\u0442\u043E\u0440\u044B\u0445 \u0436\u0438\u043B\u0438 \u0432 \u0431\u0430\u0441\u0441\u0435\u0439\u043D\u0435 \u0421\u0440\u0435\u0434\u0438\u0437\u0435\u043C\u043D\u043E\u0433\u043E \u043C\u043E\u0440\u044F (\u0432\u043D\u0435 \u0437\u0430\u0432\u0438\u0441\u0438\u043C\u043E\u0441\u0442\u0438 \u043E\u0442 \u043C\u0435\u0441\u0442\u0430 \u0438\u0445 \u043D\u044B\u043D\u0435\u0448\u043D\u0435\u0433\u043E \u043F\u0440\u043E\u0436\u0438\u0432\u0430\u043D\u0438\u044F), \u043E\u0441\u043E\u0431\u0435\u043D\u043D\u043E \u0443 \u0430\u0440\u043C\u044F\u043D, \u0435\u0432\u0440\u0435\u0435\u0432, \u0430\u0440\u0430\u0431\u043E\u0432, \u0438 \u043B\u0438\u0448\u044C \u0432 6\u00A0% \u0441\u043B\u0443\u0447\u0430\u0435\u0432 \u0443 \u043B\u0438\u0446 \u043F\u0440\u043E\u0447\u0438\u0445 \u043D\u0430\u0446\u0438\u043E\u043D\u0430\u043B\u044C\u043D\u043E\u0441\u0442\u0435\u0439."@ru . "Das Famili\u00E4re Mittelmeerfieber (FMF) \u2013 auch als famili\u00E4re rekurrente Polyserositis bezeichnet \u2013 ist eine autosomal-rezessiv vererbte Erkrankung, die geh\u00E4uft bei Bewohnern der \u00F6stlichen Mittelmeerregion (T\u00FCrkei, Nahost, Nordafrika, arabische L\u00E4nder, Armenien, seltener Griechenland und Italien) auftritt."@de . "Rodzinna gor\u0105czka \u015Br\u00F3dziemnomorska (ang. familial Mediterranean fever, FMF) \u2013 uwarunkowana genetycznie choroba zapalna, charakteryzuj\u0105ca si\u0119 epizodami gor\u0105czki z towarzysz\u0105cymi b\u00F3lami brzucha, b\u00F3lem i obrz\u0119kiem staw\u00F3w, b\u00F3lem zamostkowym. Choroba dotyczy g\u0142\u00F3wnie ludzi pochodz\u0105cych z obszaru Morza \u015Ar\u00F3dziemnego i Bliskiego Wschodu. Przyczyn\u0105 jest mutacja w genie MEFV w locus 16p13, koduj\u0105cym bia\u0142ko pyryn\u0119 (marenostryn\u0119). Dziedziczenie jest autosomalne recesywne."@pl . . "Famili\u00E6r middelhavsfeber (FMF) er en arvelig autosomal recessiv betennelsessykdom som manifesterer seg i periodiske betennelsesanfall ved ujevne mellomrom. Milj\u00F8faktorer som ser ut til \u00E5 spille en rolle er stress, utmattelse og infeksjoner. FMF er vanligst i pasientgrupper med opphav rundt Middelhavet \u2014 derav navnet. FMF er s\u00E6rlig vanlig blant armenere (opp til \u00E9n av syv har FMF), sefardiske j\u00F8der (\u00E9n av seks blant j\u00F8der av maghrebisk opprinnelse), tyrkere, druzere og libanesere og en del arabiske grupper, men finnes ogs\u00E5 bl.a. blant askenasiske j\u00F8der."@no . "Famili\u00E1rn\u00ED st\u0159edomo\u0159sk\u00E1 (st\u0159edozemn\u00ED) hore\u010Dka, \u010Di t\u00E9\u017E rodinn\u00E1 st\u0159edozemn\u00ED hore\u010Dka, je geneticky podm\u00EDn\u011Bn\u00E9 autosom\u00E1ln\u011B-recesivn\u00ED z\u00E1n\u011Btliv\u00E9 onemocn\u011Bn\u00ED zp\u016Fsoben\u00E9 mutac\u00ED genu MEFV. Postihuje pouze n\u011Bkter\u00E9 etnick\u00E9 skupiny p\u016Fvodem od St\u0159edozemn\u00EDho mo\u0159e (odtud n\u00E1zev onemocn\u011Bn\u00ED); jedn\u00E1 se konkr\u00E9tn\u011B o\u00A0Arm\u00E9ny, sefardsk\u00E9 \u017Didy, \u0158eky, Turky a Araby. K\u00A0l\u00E9\u010Db\u011B se od 70. let 20. stolet\u00ED pou\u017E\u00EDv\u00E1 kolchicin."@cs . "Das Famili\u00E4re Mittelmeerfieber (FMF) \u2013 auch als famili\u00E4re rekurrente Polyserositis bezeichnet \u2013 ist eine autosomal-rezessiv vererbte Erkrankung, die geh\u00E4uft bei Bewohnern der \u00F6stlichen Mittelmeerregion (T\u00FCrkei, Nahost, Nordafrika, arabische L\u00E4nder, Armenien, seltener Griechenland und Italien) auftritt. Hierbei handelt es sich um eine chronische Erkrankung, die durch sporadisch auftretende Fiebersch\u00FCbe mit begleitender Entz\u00FCndung der Tunica serosa charakterisiert ist, was zu Bauch-, Brust- oder Gelenkschmerzen f\u00FChrt. Die h\u00E4ufigste Komplikation des famili\u00E4ren Mittelmeerfiebers ist eine Amyloidose, wodurch sich die Lebenserwartung der Patienten verk\u00FCrzt."@de . . "Familial Mediterranean Fever"@en . . "Febbre mediterranea familiare"@it . "\u5BB6\u65CF\u6027\u5730\u4E2D\u6D77\u71B1"@ja . "Famili\u00E6r middelhavsfeber"@no . . "Famili\u00E1rn\u00ED st\u0159edomo\u0159sk\u00E1 (st\u0159edozemn\u00ED) hore\u010Dka, \u010Di t\u00E9\u017E rodinn\u00E1 st\u0159edozemn\u00ED hore\u010Dka, je geneticky podm\u00EDn\u011Bn\u00E9 autosom\u00E1ln\u011B-recesivn\u00ED z\u00E1n\u011Btliv\u00E9 onemocn\u011Bn\u00ED zp\u016Fsoben\u00E9 mutac\u00ED genu MEFV. Postihuje pouze n\u011Bkter\u00E9 etnick\u00E9 skupiny p\u016Fvodem od St\u0159edozemn\u00EDho mo\u0159e (odtud n\u00E1zev onemocn\u011Bn\u00ED); jedn\u00E1 se konkr\u00E9tn\u011B o\u00A0Arm\u00E9ny, sefardsk\u00E9 \u017Didy, \u0158eky, Turky a Araby. K\u00A0l\u00E9\u010Db\u011B se od 70. let 20. stolet\u00ED pou\u017E\u00EDv\u00E1 kolchicin."@cs . "Rodzinna gor\u0105czka \u015Br\u00F3dziemnomorska"@pl . "'\u041F\u0435\u0440\u0438\u043E\u0434\u0438\u0447\u0435\u0441\u043A\u0430\u044F \u0431\u043E\u043B\u0435\u0437\u043D\u044C \u00A0\u2014 \u0441\u0440\u0430\u0432\u043D\u0438\u0442\u0435\u043B\u044C\u043D\u043E \u0440\u0435\u0434\u043A\u043E\u0435 \u0433\u0435\u043D\u0435\u0442\u0438\u0447\u0435\u0441\u043A\u0438 \u043E\u0431\u0443\u0441\u043B\u043E\u0432\u043B\u0435\u043D\u043D\u043E\u0435 \u043D\u0430\u0441\u043B\u0435\u0434\u0441\u0442\u0432\u0435\u043D\u043D\u043E\u0435 \u0437\u0430\u0431\u043E\u043B\u0435\u0432\u0430\u043D\u0438\u0435, \u043F\u0440\u043E\u044F\u0432\u043B\u044F\u044E\u0449\u0435\u0435\u0441\u044F \u043F\u0435\u0440\u0438\u043E\u0434\u0438\u0447\u0435\u0441\u043A\u0438 \u0440\u0435\u0446\u0438\u0434\u0438\u0432\u0438\u0440\u0443\u044E\u0449\u0438\u043C \u0441\u0435\u0440\u043E\u0437\u0438\u0442\u043E\u043C \u0438 \u043E\u0442\u043D\u043E\u0441\u0438\u0442\u0435\u043B\u044C\u043D\u043E \u0447\u0430\u0441\u0442\u044B\u043C \u0440\u0430\u0437\u0432\u0438\u0442\u0438\u0435\u043C \u0430\u043C\u0438\u043B\u043E\u0438\u0434\u043E\u0437\u0430. \u0412\u0441\u0442\u0440\u0435\u0447\u0430\u0435\u0442\u0441\u044F \u043F\u0440\u0435\u0438\u043C\u0443\u0449\u0435\u0441\u0442\u0432\u0435\u043D\u043D\u043E \u0443 \u043F\u0440\u0435\u0434\u0441\u0442\u0430\u0432\u0438\u0442\u0435\u043B\u0435\u0439 \u043D\u0430\u0440\u043E\u0434\u043D\u043E\u0441\u0442\u0435\u0439, \u043F\u0440\u0435\u0434\u043A\u0438 \u043A\u043E\u0442\u043E\u0440\u044B\u0445 \u0436\u0438\u043B\u0438 \u0432 \u0431\u0430\u0441\u0441\u0435\u0439\u043D\u0435 \u0421\u0440\u0435\u0434\u0438\u0437\u0435\u043C\u043D\u043E\u0433\u043E \u043C\u043E\u0440\u044F (\u0432\u043D\u0435 \u0437\u0430\u0432\u0438\u0441\u0438\u043C\u043E\u0441\u0442\u0438 \u043E\u0442 \u043C\u0435\u0441\u0442\u0430 \u0438\u0445 \u043D\u044B\u043D\u0435\u0448\u043D\u0435\u0433\u043E \u043F\u0440\u043E\u0436\u0438\u0432\u0430\u043D\u0438\u044F), \u043E\u0441\u043E\u0431\u0435\u043D\u043D\u043E \u0443 \u0430\u0440\u043C\u044F\u043D, \u0435\u0432\u0440\u0435\u0435\u0432, \u0430\u0440\u0430\u0431\u043E\u0432, \u0438 \u043B\u0438\u0448\u044C \u0432 6\u00A0% \u0441\u043B\u0443\u0447\u0430\u0435\u0432 \u0443 \u043B\u0438\u0446 \u043F\u0440\u043E\u0447\u0438\u0445 \u043D\u0430\u0446\u0438\u043E\u043D\u0430\u043B\u044C\u043D\u043E\u0441\u0442\u0435\u0439."@ru . "La maladie p\u00E9riodique (fi\u00E8vre m\u00E9diterran\u00E9enne familiale -, ou encore maladie arm\u00E9nienne) d\u00E9signe une maladie g\u00E9n\u00E9tique autosomique r\u00E9cessive qui se manifeste notamment par des pouss\u00E9es inflammatoires survenant \u00E0 intervalles variables."@fr . . . "Familj\u00E4r medelhavsfeber (FMF) \u00E4r en autoinflammatorisk sjukdom som leder till \u00E5terkommande feberepisoder och som obehandlad kan leda till njursvikt. I Sverige finns det cirka 100 k\u00E4nda fall. Sjukdomen \u00E4r vanligare i l\u00E4nderna kring \u00F6stra medelhavet d\u00E4r f\u00F6rekomsten \u00E4r cirka 1-2 per 1000 inv\u00E5nare. Ordet familj\u00E4r kommer av att sjukdomen har en stark genetisk komponent."@sv . "med"@en . . . . . "9836"^^ . . "249100"^^ . . . "Familial Mediterranean fever"@en . . . "\u5BB6\u65CF\u6027\u5730\u4E2D\u6D77\u71B1\uFF08\u304B\u305E\u304F\u305B\u3044\u3061\u3061\u3085\u3046\u304B\u3044\u306D\u3064\u3001Familial Mediterranean fever\uFF1A\u7565\u79F0FMF\uFF09\u3068\u306F\u3001\u708E\u75C7\u6027\u306E\u907A\u4F1D\u6027\u75BE\u60A3\u306E\u4E00\u3064\u3002\u5730\u4E2D\u6D77\u5468\u8FBA\u306E\u6C11\u65CF\u306B\u7279\u306B\u591A\u3044\u3053\u3068\u304B\u3089\u547D\u540D\u3055\u308C\u3066\u3044\u308B\u304C\u3001\u305D\u308C\u4EE5\u5916\u306E\u6C11\u65CF\u3067\u3082\u767A\u75C7\u4F8B\u304C\u3042\u308B\u3002\u5BB6\u65CF\u6027\u767A\u4F5C\u6027\u591A\u6F3F\u819C\u708E\uFF08\u304B\u305E\u304F\u305B\u3044\u307B\u3063\u3055\u305B\u3044\u305F\u3057\u3087\u3046\u307E\u304F\u3048\u3093\uFF09\u3068\u3082\u3044\u3046\u3002\u81EA\u5DF1\u708E\u75C7\u75C7\u5019\u7FA4\u306E\u4E00\u3064\u3067\u3042\u308B\u3002\u306A\u304A\u5358\u306B\u300C\u5730\u4E2D\u6D77\u71B1\u300D\u3068\u3044\u3046\u3068\u30D6\u30EB\u30BB\u30E9\u75C7\u3092\u6307\u3059\u3053\u3068\u3082\u3042\u308B\u304C\u3001\u3053\u308C\u3068\u306F\u5168\u304F\u95A2\u4FC2\u306A\u3044\u3002"@ja . "Familial Mediterranean fever (FMF) is a hereditary inflammatory disorder. FMF is an autoinflammatory disease caused by mutations in MEFV, a gene which encodes a 781\u2013amino acid protein denoted pyrin."@en . . . . "\u5BB6\u65CF\u6027\u5730\u4E2D\u6D77\u71B1\uFF08\u304B\u305E\u304F\u305B\u3044\u3061\u3061\u3085\u3046\u304B\u3044\u306D\u3064\u3001Familial Mediterranean fever\uFF1A\u7565\u79F0FMF\uFF09\u3068\u306F\u3001\u708E\u75C7\u6027\u306E\u907A\u4F1D\u6027\u75BE\u60A3\u306E\u4E00\u3064\u3002\u5730\u4E2D\u6D77\u5468\u8FBA\u306E\u6C11\u65CF\u306B\u7279\u306B\u591A\u3044\u3053\u3068\u304B\u3089\u547D\u540D\u3055\u308C\u3066\u3044\u308B\u304C\u3001\u305D\u308C\u4EE5\u5916\u306E\u6C11\u65CF\u3067\u3082\u767A\u75C7\u4F8B\u304C\u3042\u308B\u3002\u5BB6\u65CF\u6027\u767A\u4F5C\u6027\u591A\u6F3F\u819C\u708E\uFF08\u304B\u305E\u304F\u305B\u3044\u307B\u3063\u3055\u305B\u3044\u305F\u3057\u3087\u3046\u307E\u304F\u3048\u3093\uFF09\u3068\u3082\u3044\u3046\u3002\u81EA\u5DF1\u708E\u75C7\u75C7\u5019\u7FA4\u306E\u4E00\u3064\u3067\u3042\u308B\u3002\u306A\u304A\u5358\u306B\u300C\u5730\u4E2D\u6D77\u71B1\u300D\u3068\u3044\u3046\u3068\u30D6\u30EB\u30BB\u30E9\u75C7\u3092\u6307\u3059\u3053\u3068\u3082\u3042\u308B\u304C\u3001\u3053\u308C\u3068\u306F\u5168\u304F\u95A2\u4FC2\u306A\u3044\u3002"@ja . . "med"@en . . . "9836"@en . "La febbre mediterranea familiare o polisierosite parossistica familiare \u00E8 una malattia genetica a trasmissione autosomica recessiva, caratterizzata da febbre ricorrente associata a peritonite o pleurite, pi\u00F9 frequente tra le popolazioni originarie del mar Mediterraneo."@it . "Famili\u00E6r middelhavsfeber (FMF) er en arvelig autosomal recessiv betennelsessykdom som manifesterer seg i periodiske betennelsesanfall ved ujevne mellomrom. Milj\u00F8faktorer som ser ut til \u00E5 spille en rolle er stress, utmattelse og infeksjoner. FMF er vanligst i pasientgrupper med opphav rundt Middelhavet \u2014 derav navnet."@no . "La maladie p\u00E9riodique (fi\u00E8vre m\u00E9diterran\u00E9enne familiale -, ou encore maladie arm\u00E9nienne) d\u00E9signe une maladie g\u00E9n\u00E9tique autosomique r\u00E9cessive qui se manifeste notamment par des pouss\u00E9es inflammatoires survenant \u00E0 intervalles variables. Le caract\u00E8re h\u00E9r\u00E9ditaire de cette maladie est av\u00E9r\u00E9 depuis longtemps, sa fr\u00E9quence est \u00E9lev\u00E9e chez les sujets originaires du pourtour m\u00E9diterran\u00E9en (populations juives du Maghreb -environ une personne sur six est porteuse du g\u00E8ne mutant-, arm\u00E9niens, certaines populations turques druzes et arabes). Cependant, la notion familiale est de plus en plus rarement retrouv\u00E9e du fait du mode de transmission r\u00E9cessif. Des cas de transmission pseudo-dominantes ont toutefois fait l'objet de plusieurs \u00E9tudes. Des facteurs environnementaux peuvent \u00E9galement intervenir, chez certaines personnes, dans le d\u00E9clenchement de telles crises\u00A0: p\u00E9riodes de stress, fatigue, infections. Le diagnostic se fait g\u00E9n\u00E9ralement par \u00E9limination, g\u00E9n\u00E9ralement selon les crit\u00E8res de Sohar. En France, plusieurs laboratoires permettent de proc\u00E9der \u00E0 un diagnostic g\u00E9n\u00E9tique."@fr . . "Familial Mediterranean Fever"@en . . . . "Rodzinna gor\u0105czka \u015Br\u00F3dziemnomorska (ang. familial Mediterranean fever, FMF) \u2013 uwarunkowana genetycznie choroba zapalna, charakteryzuj\u0105ca si\u0119 epizodami gor\u0105czki z towarzysz\u0105cymi b\u00F3lami brzucha, b\u00F3lem i obrz\u0119kiem staw\u00F3w, b\u00F3lem zamostkowym. Choroba dotyczy g\u0142\u00F3wnie ludzi pochodz\u0105cych z obszaru Morza \u015Ar\u00F3dziemnego i Bliskiego Wschodu. Przyczyn\u0105 jest mutacja w genie MEFV w locus 16p13, koduj\u0105cym bia\u0142ko pyryn\u0119 (marenostryn\u0119). Dziedziczenie jest autosomalne recesywne."@pl . . . . . . "Maladie p\u00E9riodique"@fr . "Familial Mediterranean fever (FMF) is a hereditary inflammatory disorder. FMF is an autoinflammatory disease caused by mutations in MEFV, a gene which encodes a 781\u2013amino acid protein denoted pyrin. The disorder has been given various names including familial paroxysmal polyserositis, periodic peritonitis, recurrent polyserositis, benign paroxysmal peritonitis, periodic disease or periodic fever, Reimann periodic disease or Reimann's syndrome, Siegal-Cattan-Mamou disease, and Wolff periodic disease. Note that \"periodic fever\" can also refer to any of the Periodic fever syndromes."@en . "1410"^^ . "Familj\u00E4r medelhavsfeber (FMF) \u00E4r en autoinflammatorisk sjukdom som leder till \u00E5terkommande feberepisoder och som obehandlad kan leda till njursvikt. I Sverige finns det cirka 100 k\u00E4nda fall. Sjukdomen \u00E4r vanligare i l\u00E4nderna kring \u00F6stra medelhavet d\u00E4r f\u00F6rekomsten \u00E4r cirka 1-2 per 1000 inv\u00E5nare. Ordet familj\u00E4r kommer av att sjukdomen har en stark genetisk komponent."@sv . "\u041F\u0435\u0440\u0438\u043E\u0434\u0438\u0447\u0435\u0441\u043A\u0430\u044F \u0431\u043E\u043B\u0435\u0437\u043D\u044C"@ru . . . "D010505"@en . . "D010505"@en . .